{"id":10237,"date":"2023-12-14T20:56:18","date_gmt":"2023-12-14T20:56:18","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/?p=10237"},"modified":"2025-12-30T19:09:58","modified_gmt":"2025-12-30T19:09:58","slug":"budd-chiari-syndrome","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/budd-chiari-syndrome\/","title":{"rendered":"Factores de Riesgo del S\u00edndrome de Budd-Chiari"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>El s\u00edndrome primario de Budd-Chiari se caracteriza por un tracto de salida venoso hep\u00e1tico bloqueado en varios niveles, desde las peque\u00f1as venas hep\u00e1ticas hasta la vena cava inferior, como resultado de una trombosis o sus secuelas fibrosas. Esta rara enfermedad afecta principalmente a adultos j\u00f3venes. Se han identificado m\u00faltiples factores de riesgo que a menudo se combinan en el mismo paciente.<!--more--><\/p>\n<p><strong>Propuesta de trabajo para investigar los factores de riesgo subyacentes del s\u00edndrome de Budd-Chiari<\/strong><\/p>\n<p>A. En todos los pacientes<\/p>\n<ul>\n<li>Historia personal y familiar de trombosis venosa profunda espont\u00e1nea recurrente.<\/li>\n<li>Uso de anticonceptivos orales en pacientes femeninas.<\/li>\n<li>Mutaci\u00f3n V617F JAK 2 en granulocitos de sangre perif\u00e9rica. Cuando la mutaci\u00f3n no se detecta, se realiza una biopsia de m\u00e9dula \u00f3sea en busca de grupos de megacariocitos distr\u00f3ficos (enfermedades mieloproliferativas)<\/li>\n<li>Citometr\u00eda de flujo para c\u00e9lulas sangu\u00edneas deficientes en CD55 y CD59 (hemoglobinuria parox\u00edstica nocturna)<\/li>\n<li>Resistencia a la prote\u00edna C activada. Cuando presente prueba molecular para mutaci\u00f3n del Factor V Leiden<\/li>\n<li>Prueba molecular para la mutaci\u00f3n del gen de protrombina G20210A<\/li>\n<li>Anticoagulante l\u00fapico, anticuerpos anti-glucoprote\u00edna-1 beta2, anticuerpos anticardiolipina (s\u00edndrome antifosfol\u00edpido)<\/li>\n<\/ul>\n<p>B. En pacientes sin disfunci\u00f3n hep\u00e1tica marcada (nivel de protrombina normal)<\/p>\n<ul>\n<li>Niveles plasm\u00e1ticos de prote\u00edna C, prote\u00edna S y antitrombina.<\/li>\n<li>Niveles plasm\u00e1ticos de homociste\u00edna<\/li>\n<\/ul>\n<p>C- En pacientes con antecedentes familiares o personales de trombosis venosa profunda espont\u00e1nea recurrente: derivar al especialista en coagulaci\u00f3n sangu\u00ednea para estudio detallado<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li>Garcia-Pag\u00e1n JC, Valla DC. Primary Budd-Chiari Syndrome. N Engl J Med. 2023 Apr 6;388(14):1307-1316. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/37018494\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<li>Valla DC. Primary Budd-Chiari syndrome. J Hepatol. 2009 Jan;50(1):195-203. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/19012988\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Dic 14, 2023.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>El s\u00edndrome primario de Budd-Chiari se caracteriza por un tracto de salida venoso hep\u00e1tico bloqueado en varios niveles, desde las peque\u00f1as venas hep\u00e1ticas hasta la vena cava inferior, como resultado de una trombosis o sus secuelas fibrosas. Esta rara enfermedad afecta principalmente a adultos j\u00f3venes. Se han identificado m\u00faltiples factores de riesgo que a menudo &#8230; <a title=\"Factores de Riesgo del S\u00edndrome de Budd-Chiari\" class=\"read-more\" href=\"https:\/\/medicalcriteria.com\/web\/es\/budd-chiari-syndrome\/\" aria-label=\"Leer m\u00e1s sobre Factores de Riesgo del S\u00edndrome de Budd-Chiari\">Leer m\u00e1s<\/a><\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"footnotes":""},"categories":[171],"tags":[2634,2635,1893,1894,836,767,5,4],"class_list":["post-10237","post","type-post","status-publish","format-standard","hentry","category-hematology","tag-budd","tag-chiari","tag-factores","tag-factors","tag-riesgo","tag-risk","tag-sindrome","tag-syndrome"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Factores de Riesgo del S\u00edndrome de Budd-Chiari - MedicalCRITERIA.com<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/medicalcriteria.com\/web\/budd-chiari-syndrome\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"[:es]Factores de Riesgo del S\u00edndrome de Budd-Chiari[:en]Risk Factors of Budd-Chiari Syndrome[:] - MedicalCRITERIA.com\" \/>\n<meta property=\"og:description\" content=\"El s\u00edndrome primario de Budd-Chiari se caracteriza por un tracto de salida venoso hep\u00e1tico bloqueado en varios niveles, desde las peque\u00f1as venas hep\u00e1ticas hasta la vena cava inferior, como resultado de una trombosis o sus secuelas fibrosas. 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