{"id":2112,"date":"2019-10-09T22:43:30","date_gmt":"2019-10-09T22:43:30","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/?p=2232"},"modified":"2026-01-28T19:02:26","modified_gmt":"2026-01-28T19:02:26","slug":"vogt-koyanagi-harada","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/vogt-koyanagi-harada\/","title":{"rendered":"Criterios Diagn\u00f3stico Revisados de la Enfermedad de Vogt-Koyanagi-Harada (EVKH)"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>La enfermedad de Vogt-Koyanagi-Harada (EVKH) es una panuve\u00edtis granulomatosa cr\u00f3nica bilateral asociada con manifestaciones del sistema nervioso central, auditivo y tegumentarias.<!--more--><br \/>\nCl\u00e1sicamente, la enfermedad comienza con una fase prodr\u00f3mica de s\u00edntomas neuroauditivos, seguida de una fase de uve\u00edtis aguda y, finalmente, las manifestaciones de la etapa cr\u00f3nica.<\/p>\n<p><strong>Criterios Diagn\u00f3stico Revisados de la Enfermedad de Vogt-Koyanagi-Harada (EVKH)<\/strong><\/p>\n<p>El diagn\u00f3stico de EVKH se basa principalmente en caracter\u00edsticas cl\u00ednicas. La American Uveitis Society (AUS) adopt\u00f3 los siguientes criterios de diagn\u00f3stico:<\/p>\n<ul>\n<li>Sin antecedentes de traumatismo ocular y\/o cirug\u00eda;<\/li>\n<li>Al menos tres de los siguientes cuatro signos:\n<ol style=\"list-style-type: lower-alpha;\">\n<li>Iridociclitis cr\u00f3nica bilateral;<\/li>\n<li>Uve\u00edtis posterior (desprendimientos de retina multifocales exudativos o de epitelio pigmentario retiniano (EPR)); hiperemia o edema de papila; o \u00abfondo en puesta de sol\u00bb, que es una apariencia de fondo amarillo-naranja debido a la despigmentaci\u00f3n de EPR y coroides;<\/li>\n<li>Signos neurol\u00f3gicos (tinnitus, rigidez del cuello, s\u00edntomas del sistema nervioso central o nervios craneales o\u00a0pleocitosis del l\u00edquido cefalorraqu\u00eddeo);<\/li>\n<li>Hallazgos cut\u00e1neos (alopecia, poliosis o vitiligo).<\/li>\n<\/ol>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p><strong>Criterios de diagn\u00f3stico revisados de la enfermedad de Vogt-Koyanagi-Harada propuestos por el Comit\u00e9 Internacional de Nomenclatura<\/strong><\/p>\n<ol>\n<li>Sin antecedentes de traumatismo ocular penetrante o cirug\u00eda previa al inicio de la uve\u00edtis.<\/li>\n<li>Sin evidencia cl\u00ednica o de laboratorio que sugiera otras entidades de enfermedad ocular.<\/li>\n<li>Compromiso ocular bilateral (se debe cumplir a o b, dependiendo de la etapa de la enfermedad cuando se examina al paciente):\n<ol style=\"list-style-type: lower-alpha;\">\n<li>Manifestaciones tempranas de la enfermedad:\n<ol style=\"list-style-type: upper-roman;\">\n<li>Evidencia de coroiditis difusa (con o sin uve\u00edtis anterior, reacci\u00f3n inflamatoria v\u00edtrea o hiperemia de la papila), que puede manifestarse como (A) \u00e1reas focales de l\u00edquido subretiniano, o (B) desprendimientos retinianos exudativos bullosos.<\/li>\n<li>Si se encuentran resultados dudosos en el fondo de ojo, ambos:\n<ol style=\"list-style-type: upper-alpha;\">\n<li>Angiograf\u00eda con fluoresce\u00edna que muestra perfusi\u00f3n coroidea focal retardada, m\u00faltiples \u00e1reas puntuales de fuga, grandes \u00e1reas placoides de hiperfluorescencia, agrupaci\u00f3n dentro del l\u00edquido subretiniano y tinci\u00f3n del nervio \u00f3ptico;<\/li>\n<li>ultrasonido que muestra engrosamiento coroideo difuso sin evidencia de escleritis posterior.<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<\/li>\n<li>Manifestaciones tard\u00edas de enfermedad:\n<ol style=\"list-style-type: upper-roman;\">\n<li>Historia sugestiva de presencia previa de hallazgos tempranos observados en 3a y (II) o (III) m\u00e1s abajo, o m\u00faltiples signos de (III) m\u00e1s abajo:<\/li>\n<li>Despigmentaci\u00f3n ocular: (A) fondo de ojo de color anaranjado en \u00abpuesta de sol\u00bb (sunset glow fundus) o (B) signo de Sugiura (despigmentaci\u00f3n del limbo esclerocorneal).<\/li>\n<li>Otros signos oculares incluyen (A) cicatrices despigmentadas coriorretinianas numulares, o (B) aglomeraci\u00f3n y\/o migraci\u00f3n del epitelio pigmentario de la retina, o (C) uve\u00edtis anterior cr\u00f3nica o recurrente.<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<\/li>\n<li>Hallazgos neurol\u00f3gicos\/auditivos (pueden resolverse con el tiempo de la evaluaci\u00f3n):\n<ol style=\"list-style-type: lower-alpha;\">\n<li>Meningismo (malestar, fiebre, dolor de cabeza, n\u00e1useas, dolor abdominal, rigidez del cuello y la espalda, o una combinaci\u00f3n de estos factores); tenga en cuenta que el dolor de cabeza por s\u00ed solo no es suficiente para cumplir con la definici\u00f3n de meningismo.<\/li>\n<li>Ac\u00fafenos o tinnitus<\/li>\n<li>Pleocitosis del l\u00edquido cefalorraqu\u00eddeo<\/li>\n<\/ol>\n<\/li>\n<li>Hallazgos tegumentarios (sin aparici\u00f3n previa de enfermedad del sistema nervioso central u ocular):\n<ol style=\"list-style-type: lower-alpha;\">\n<li>Alopecia, o<\/li>\n<li>Poliosis, o<\/li>\n<li>V\u00edtiligo.<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<p><strong>EVKH Completa:<\/strong> los criterios 1-5 deben estar presentes<br \/>\n<strong>EVKH Incompleta:<\/strong> criterios 1-3 y 4 o 5 deben estar presentes<br \/>\n<strong>EVKH Probable (enfermedad ocular aislada):<\/strong> los criterios 1-3 deben estar presentes<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li>Burkholder BM. Vogt-Koyanagi-Harada disease.\u00a0Curr Opin Ophthalmol. 2015 Nov;26(6):506-11. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/26448042\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Lavezzo MM, Sakata VM, Morita C, Rodriguez EE, Abdallah SF, da Silva FT, Hirata CE, Yamamoto JH. Vogt-Koyanagi-Harada disease: review of a rare autoimmune disease targeting antigens of melanocytes.\u00a0Orphanet J Rare Dis. 2016 Mar 24;11:29. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/27008848\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>O&#8217;Keefe GA, Rao NA. Vogt-Koyanagi-Harada disease.\u00a0Surv Ophthalmol. 2017 Jan &#8211; Feb;62(1):1-25. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/27241814\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Karti O, Ayhan Z, Saatci OA. Use of Imaging Modalities in Vogt-Koyanagi-Harada Disease: An Overview. Cesk Slov Oftalmol. 2025;81(5):223-231. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/40705535\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Oct 02, 2019.<br \/>\nActualizado Ene 28, 2026.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>La enfermedad de Vogt-Koyanagi-Harada (EVKH) es una panuve\u00edtis granulomatosa cr\u00f3nica bilateral asociada con manifestaciones del sistema nervioso central, auditivo y tegumentarias.<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[45],"tags":[16,15,14,13,51,50,48,47,8,7,52,49,46],"class_list":["post-2112","post","type-post","status-publish","format-standard","hentry","category-rheumatology","tag-criteria","tag-criterios","tag-diagnostic","tag-diagnostico","tag-disease","tag-enfermedad","tag-harada","tag-koyanagi","tag-revisados","tag-revised","tag-vkh","tag-vkhd","tag-vogt"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - 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