{"id":2317,"date":"2017-01-12T15:31:16","date_gmt":"2017-01-12T15:31:16","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/gaspsc\/"},"modified":"2026-03-10T19:45:36","modified_gmt":"2026-03-10T19:45:36","slug":"gaspsc","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/gaspsc\/","title":{"rendered":"Criterios Diagn\u00f3stico de la Colangitis Esclerosante Primaria (CEP)"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>La colangitis esclerosante primaria (CEP) es una enfermedad hep\u00e1tica colest\u00e1sica cr\u00f3nica de causa desconocida que se caracteriza patol\u00f3gicamente por un proceso inflamatorio y fibr\u00f3tico centrado en el epitelio, conduciendo a estenosis biliar difusa y aumento del espesor de pared a trav\u00e9s de los \u00e1rboles biliares intra y extrahep\u00e1ticos.<br \/>\n<!--more--><br \/>\n<b>Criterios diagn\u00f3stico de la colangitis esclerosante primaria (CEP)<\/b><br \/>\nEs necesario excluir la colangitis esclerosante relacionada con IgG4, colangitis esclerosante secundarias causada por enfermedades con una patog\u00e9nesis obvia y enfermedades malignas como el c\u00e1ncer biliar.<br \/>\nA. Items diagn\u00f3stico<br \/>\nI. Items principales<br \/>\nA. Im\u00e1genes de las v\u00edas biliares<br \/>\n1) Hallazgos colangiogr\u00e1ficos caracter\u00edsticos de CEP<br \/>\n2) Hallazgos colangiogr\u00e1ficos no espec\u00edficos del CEP<br \/>\nB. Incremento del nivel de fosfatasa alcalina<br \/>\nII. Items menores<br \/>\na. Asociaci\u00f3n con enfermedad inflamatoria intestinal<br \/>\nb. Histolog\u00eda del h\u00edgado: colangitis fibrosa \/ lesi\u00f3n en piel de cebolla<br \/>\nB. Diagn\u00f3stico<br \/>\nDiagn\u00f3stico definitivo<\/p>\n<ul>\n<li>A1) + B<\/li>\n<li>A1) + a<\/li>\n<li>A1) + b<\/li>\n<li>A2) + B + a + b<\/li>\n<\/ul>\n<p>Diagn\u00f3stico probable<\/p>\n<ul>\n<li>A1)<\/li>\n<li>A2) + B + a<\/li>\n<li>A2) + B + b<\/li>\n<li>A2) + a + b<\/li>\n<\/ul>\n<p>Diagn\u00f3stico posible<\/p>\n<ul>\n<li>A2) + a<\/li>\n<li>A2) + b<\/li>\n<\/ul>\n<p><b>Listas de colangitis esclerosante secundaria<\/b><br \/>\nCong\u00e9nito<\/p>\n<ul>\n<li>Enfermedad de Caroli<\/li>\n<li>Fibrosis qu\u00edstica<\/li>\n<\/ul>\n<p>Obstrucci\u00f3n cr\u00f3nica<\/p>\n<ul>\n<li>Coledocolitiasis<\/li>\n<li>Estrecheces biliares (secundario a trauma quir\u00fargico, pancreatitis cr\u00f3nica)<\/li>\n<li>Estrecheces anastom\u00f3ticas del injerto hep\u00e1tico<\/li>\n<li>Neoplasias (benignas, malignas, metast\u00e1sicas)<\/li>\n<\/ul>\n<p>Infeccioso<\/p>\n<ul>\n<li>Colangitis bacteriana<\/li>\n<li>Colangitis piog\u00e9nica recurrente<\/li>\n<li>Infecci\u00f3n parasitaria (criptosporidiosis, microsporidiosis)<\/li>\n<li>Infecci\u00f3n por citomegalovirus<\/li>\n<\/ul>\n<p>T\u00f3xico<\/p>\n<ul>\n<li>Alcohol accidental, formaldeh\u00eddo, instilaci\u00f3n salina hipert\u00f3nica en conductos biliares<\/li>\n<\/ul>\n<p>Inmunol\u00f3gico<\/p>\n<ul>\n<li>Colangitis eosinof\u00edlica<\/li>\n<li>Inmunodeficiencia adquirida<\/li>\n<\/ul>\n<p>Isqu\u00e9mico<\/p>\n<ul>\n<li>Trauma vascular<\/li>\n<li>Colangitis esclerosante postraum\u00e1tica<\/li>\n<li>Trombosis de la arteria hep\u00e1tica postrasplante<\/li>\n<li>Rechazo del aloinjerto hep\u00e1tico (agudo, cr\u00f3nico)<\/li>\n<li>Lesi\u00f3n intraarterial relacionada con la quimioterapia<\/li>\n<li>Terapia de embolizaci\u00f3n arterial transcat\u00e9ter<\/li>\n<\/ul>\n<p>Trastornos infiltrantes<\/p>\n<ul>\n<li>Vasculitis sist\u00e9mica<\/li>\n<li>Amiloidosis<\/li>\n<li>Lesi\u00f3n por radiaci\u00f3n<\/li>\n<li>Sarcoidosis<\/li>\n<li>Mastocitosis sist\u00e9mica<\/li>\n<li>S\u00edndrome hipereosinof\u00edlico<\/li>\n<li>Enfermedad de Hodgkin<\/li>\n<\/ul>\n<div><\/div>\n<p><b>Bibliograf\u00eda:<\/b><\/p>\n<ol>\n<li>Nakazawa T, Notohara K, Tazuma S, Tanaka A, Isayama H, Tsuyuguchi T, Mori T, Takikawa H. The 2016 diagnostic criteria for primary sclerosing cholangitis. J Gastroenterol. 2016 Dec 5.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/27921168\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Lazaridis KN, LaRusso NF. Primary Sclerosing Cholangitis. N Engl J Med. 2016 Sep 22;375(12):1161-70.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/27653566\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Nakazawa T, Naitoh I, Hayashi K, Miyabe K, Simizu S, Joh T. Diagnosis of IgG4-related sclerosing cholangitis.\u00a0World J Gastroenterol. 2013 Nov 21;19(43):7661-70.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/24282356\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Svensson Di Giorgio S, Scandavini CM, Molinaro A, Arnelo U, Valente R. Primary Sclerosing Cholangitis: Diagnosis, Management, and Clinical Challenges. J Clin Med. 2026 Feb 2;15(3):1149. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/41682828\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Ene 12, 2017.<br \/>\nActualizado Mar 10, 2026.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>La colangitis esclerosante primaria (CEP) es una enfermedad hep\u00e1tica colest\u00e1sica cr\u00f3nica de causa desconocida que se caracteriza patol\u00f3gicamente por un proceso inflamatorio y fibr\u00f3tico centrado en el epitelio, conduciendo a estenosis biliar difusa y aumento del espesor de pared a trav\u00e9s de los \u00e1rboles biliares intra y extrahep\u00e1ticos.<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[53],"tags":[661,376,375,16,15,14,13,660,282,114,659,662],"class_list":["post-2317","post","type-post","status-publish","format-standard","hentry","category-gastroenterology","tag-cep","tag-cholangitis","tag-colangitis","tag-criteria","tag-criterios","tag-diagnostic","tag-diagnostico","tag-esclerosante","tag-primaria","tag-primary","tag-psc","tag-sclerosing"],"modified_by":"Guillermo Firman","_links":{"self":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/2317","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/comments?post=2317"}],"version-history":[{"count":4,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/2317\/revisions"}],"predecessor-version":[{"id":10693,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/2317\/revisions\/10693"}],"wp:attachment":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/media?parent=2317"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/categories?post=2317"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/tags?post=2317"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}