{"id":2334,"date":"2015-09-18T15:49:29","date_gmt":"2015-09-18T15:49:29","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/hethl\/"},"modified":"2026-03-18T19:35:09","modified_gmt":"2026-03-18T19:35:09","slug":"hethl","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/hethl\/","title":{"rendered":"Clasificaci\u00f3n de la OMS de Tumores Hematopoy\u00e9ticos y de Tejidos Linfoides"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>La clasificaci\u00f3n de la Organizaci\u00f3n Mundial de la Salud (OMS) de las neoplasias linfoides, actualizado en 2008, representa un consenso mundial sobre el diagn\u00f3stico de estos tumores y se basa en el reconocimiento de enfermedades distintas, utilizando un enfoque multidisciplinario.<br \/>\n<!--more--><br \/>\n<b>Clasificaci\u00f3n de la OMS de Tumores Hematopoy\u00e9ticos y de Tejidos Linfoides\u00a0<\/b><br \/>\n<b>Neoplasias de c\u00e9lulas B maduras<\/b><\/p>\n<ul>\n<li>Leucemia linfoc\u00edtica cr\u00f3nica \/ linfoma linfoc\u00edtico peque\u00f1o<\/li>\n<li>Leucemia prolinfoc\u00edtica de c\u00e9lulas B<\/li>\n<li>Linfoma espl\u00e9nico de la zona marginal<\/li>\n<li>Leucemia de c\u00e9lulas pilosas<\/li>\n<li>Linfoma espl\u00e9nico \/ leucemia, inclasificable*<\/li>\n<\/ul>\n<p>-Linfoma espl\u00e9nico de c\u00e9lulas B peque\u00f1as con infiltraci\u00f3n difusa de la pulpa roja*<br \/>\n-Variante de la leucemia de c\u00e9lulas peludas*<\/p>\n<ul>\n<li>Linfoma linfoplasmoc\u00edtico<\/li>\n<\/ul>\n<p>-Macroglobulinemia de Waldenstr\u00f6m<\/p>\n<ul>\n<li>Enfermedades de cadenas pesadas<\/li>\n<\/ul>\n<p>-Enfermedad de cadena pesada alfa<br \/>\n-Enfermedad de cadena pesada gamma<br \/>\n-Enfermedad de cadena pesada mu<\/p>\n<ul>\n<li>Mieloma de c\u00e9lulas plasm\u00e1ticas<\/li>\n<li>Plasmocitoma solitario del hueso<\/li>\n<li>Plasmocitoma extra\u00f3seo<\/li>\n<li>Linfoma extranodal de la zona marginal del tejido linfoide asociado a las mucosas (linfoma MALT)<\/li>\n<li>Linfoma de la zona marginal nodal<\/li>\n<\/ul>\n<p>-Linfoma de la zona marginal\u00a0nodal pedi\u00e1trico*<\/p>\n<ul>\n<li>Linfoma folicular<\/li>\n<\/ul>\n<p>-Linfoma folicular pedi\u00e1trico*<\/p>\n<ul>\n<li>Linfoma cut\u00e1neo Primario centro-fol\u00edcular<\/li>\n<li>Linfoma de c\u00e9lulas del manto<\/li>\n<li>Linfoma difuso de c\u00e9lulas B grandes (DLBCL), NOS<\/li>\n<\/ul>\n<p>-Linfoma de c\u00e9lulas B grandes rica en\u00a0c\u00e9lulas -T \/ histiocitos<br \/>\n-DLBCL primario\u00a0del SNC<br \/>\n-DLBCL\u00a0Cut\u00e1neo\u00a0Primario, tipo de la pierna<br \/>\n-DLBCL\u00a0EBV-positivo de los ancianos*<\/p>\n<ul>\n<li>DLBCL asociado con inflamaci\u00f3n cr\u00f3nica<\/li>\n<li>Granulomatosis linfomatoide<\/li>\n<li>Linfoma de c\u00e9lulas B grandes mediastinal primario (t\u00edmico)<\/li>\n<li>Linfoma de c\u00e9lulas B grandes intravascular<\/li>\n<li>Linfoma de c\u00e9lulas B grandes ALK-positivo<\/li>\n<li>Linfoma plasmabl\u00e1stico<\/li>\n<li>Linfoma de c\u00e9lulas B grandes a partir de la\u00a0enfermedad de Castleman multic\u00e9ntrica\u00a0asociado a\u00a0HHV8<\/li>\n<li>Linfoma de efusi\u00f3n primaria<\/li>\n<li>Linfoma de Burkitt<\/li>\n<li>Linfoma de c\u00e9lulas B, inclasificable, con caracter\u00edsticas intermedias entre el linfoma de\u00a0c\u00e9lulas B grandes\u00a0difuso y el linfoma de Burkitt<\/li>\n<li>Linfoma de c\u00e9lulas B, inclasificable, con caracter\u00edsticas intermedias entre el linfoma\u00a0de c\u00e9lulas B grandes\u00a0difuso y el linfoma de Hodgkin cl\u00e1sico<\/li>\n<\/ul>\n<p><b>C\u00e9lulas T\u00a0<\/b><b>Maduras y\u00a0<\/b><b>neoplasias\u00a0<\/b><b>de c\u00e9lulas NK<\/b><\/p>\n<ul>\n<li>Leucemia prolinfoc\u00edtica de c\u00e9lulas T<\/li>\n<li>Leucemia linfoc\u00edtica\u00a0granular de c\u00e9lulas T grandes<\/li>\n<li>Trastorno linfoproliferativo cr\u00f3nico de c\u00e9lulas NK*<\/li>\n<li>Leucemia agresiva\u00a0de c\u00e9lulas NK<\/li>\n<li>Enfermedad linfoproliferativa de c\u00e9lulas T con\u00a0virus Epstein-Barr\u00a0positivo sist\u00e9mica de la infancia<\/li>\n<li>Linfoma simil\u00a0vacciniforme hidroa<\/li>\n<li>Leucemia\/linfoma\u00a0de c\u00e9lulas T del adulto<\/li>\n<li>Linfoma extranodal\u00a0de las c\u00e9lulas T\/NK, tipo nasal<\/li>\n<li>Linfoma de c\u00e9lulas T\u00a0asociada a enteropat\u00eda<\/li>\n<li>Linfoma de c\u00e9lulas T hepatoespl\u00e9nico<\/li>\n<li>Linfoma de c\u00e9lulas T simil\u00a0paniculitis subcut\u00e1nea<\/li>\n<li>Micosis fungoide<\/li>\n<li>S\u00edndrome de S\u00e9zary<\/li>\n<li>Trastornos linfoproliferativos\u00a0de c\u00e9lulas T CD30+ cut\u00e1neo primario<\/li>\n<\/ul>\n<p>-Papulosis linfomatoide<br \/>\n-Linfoma de c\u00e9lulas grandes\u00a0anapl\u00e1sico cut\u00e1neo primario<\/p>\n<ul>\n<li>Linfoma de c\u00e9lulas T\u00a0gamma-delta cut\u00e1neo primario<\/li>\n<li>Linfoma de c\u00e9lulas T citot\u00f3xicas epidermotr\u00f3pico agresivo CD8+ cut\u00e1neo primario*<\/li>\n<li>Linfoma de c\u00e9lulas T\u00a0peque\u00f1o\/mediano\u00a0CD4+ cut\u00e1neo primario*<\/li>\n<li>Linfoma de c\u00e9lulas T\u00a0perif\u00e9rico, NOS<\/li>\n<li>Linfoma de c\u00e9lulas T angioinmunobl\u00e1stico<\/li>\n<li>Linfoma de c\u00e9lulas grandes anapl\u00e1sico, ALK-positivo<\/li>\n<li>Linfoma de c\u00e9lulas grandes anapl\u00e1sico, ALK-negativo*<\/li>\n<\/ul>\n<p><b>Linfoma de Hodgkin<\/b><\/p>\n<ul>\n<li>Linfoma de Hodgkin con\u00a0predominio linfocito nodular<\/li>\n<li>Linfoma de Hodgkin cl\u00e1sico<\/li>\n<li>Linfoma de Hodgkin cl\u00e1sico esclerosis nodular<\/li>\n<li>Linfoma de Hodgkin cl\u00e1sico rico en linfocitos<\/li>\n<li>Linfoma de Hodgkin cl\u00e1sico celularidad mixta<\/li>\n<li>Linfoma de Hodgkin cl\u00e1sico con depleci\u00f3n de linfocitos<\/li>\n<\/ul>\n<p><b>Neoplasias de c\u00e9lulas dendr\u00edticas e h<\/b><b>istioc\u00edticas\u00a0<\/b><\/p>\n<ul>\n<li>Sarcoma histioc\u00edtico<\/li>\n<li>Histiocitosis de c\u00e9lulas de Langerhans<\/li>\n<li>Sarcoma de c\u00e9lulas de Langerhans<\/li>\n<li>Sarcoma de c\u00e9lulas dendr\u00edticas interdigitantes<\/li>\n<li>Sarcoma de c\u00e9lulas dendr\u00edticas foliculares<\/li>\n<li>Tumor de c\u00e9lulas reticulares fibrobl\u00e1stica<\/li>\n<li>Tumor de c\u00e9lulas dendr\u00edticas intermedio<\/li>\n<li>Xantogranuloma juvenil diseminada<\/li>\n<\/ul>\n<p><b>Trastornos linfoproliferativos postrasplante (ELPT)<\/b><\/p>\n<ul>\n<li>Lesiones tempranas<\/li>\n<\/ul>\n<p>-Hiperplasia plasmac\u00edtica<br \/>\n-Mononucleosis infecciosa\u00a0s\u00edmil\u00a0PTLD<\/p>\n<ul>\n<li>PTLD polim\u00f3rfica<\/li>\n<li>PTLD monom\u00f3rfica (tipos de c\u00e9lulas T\/NK y B) \u2020<\/li>\n<li>Linfoma Hodgkin\u00a0Cl\u00e1sico tipo PTLD \u2020<\/li>\n<\/ul>\n<p>NOS indica que no se especifique lo contrario; ALK, quinasa de linfoma anapl\u00e1sico; HHV8, virus del herpes humano 8; y NK, natural killer.<br \/>\n* Estos tipos histol\u00f3gicos son entidades provisionales para las que el Grupo de Trabajo OMS sent\u00eda que no hab\u00eda pruebas suficientes para reconocer como enfermedades distintas hasta el momento.<br \/>\n\u2020 Estas lesiones se clasifican de acuerdo con la leucemia o el linfoma al que corresponden.<\/p>\n<p>&nbsp;<\/p>\n<p><b>Bibliograf\u00eda:<\/b><\/p>\n<ol>\n<li>Campo E, Swerdlow SH, Harris NL, Pileri S, Stein H, Jaffe ES. The 2008 WHO classification of lymphoid neoplasms and beyond: evolving concepts and practical applications.\u00a0Blood. 2011 May 12;117(19):5019-32.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/21300984\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Vardiman JW, Thiele J, Arber DA, Brunning RD, Borowitz MJ, Porwit A, Harris NL, Le Beau MM, Hellstr\u00f6m-Lindberg E, Tefferi A, Bloomfield CD. The 2008 revision of the World Health Organization (WHO) classification of myeloid neoplasms and acute leukemia: rationale and important changes.\u00a0Blood. 2009 Jul 30;114(5):937-51.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/19357394\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Thiele J, Kvasnicka HM, Orazi A, Gianelli U, Gangat N, Vannucchi AM, Barbui T, Arber DA, Tefferi A. The international consensus classification of myeloid neoplasms and acute Leukemias: myeloproliferative neoplasms. Am J Hematol. 2023 Jan;98(1):166-179. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/36200127\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Nov 12, 2015.<br \/>\nActualizado Mar 18, 2026.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>La clasificaci\u00f3n de la Organizaci\u00f3n Mundial de la Salud (OMS) de las neoplasias linfoides, actualizado en 2008, representa un consenso mundial sobre el diagn\u00f3stico de estos tumores y se basa en el reconocimiento de enfermedades distintas, utilizando un enfoque multidisciplinario.<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[171],"tags":[166,167,751,750,749,748,747,746,745,744,306],"class_list":["post-2334","post","type-post","status-publish","format-standard","hentry","category-hematology","tag-clasificacion","tag-classification","tag-hematopoietic","tag-hematopoyeticos","tag-linfoides","tag-lymphoid","tag-tejidos","tag-tissues","tag-tumores","tag-tumors","tag-who"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - 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