{"id":2355,"date":"2014-11-06T15:43:12","date_gmt":"2014-11-06T15:43:12","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/hemth\/"},"modified":"2026-10-29T19:35:28","modified_gmt":"2026-10-29T19:35:28","slug":"hemth","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/hemth\/","title":{"rendered":"Caracter\u00edsticas de las Talasemias"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>Las talasemias son un grupo de trastornos hematol\u00f3gicos hereditarios causados por defectos en la s\u00edntesis de una o m\u00e1s de las cadenas de hemoglobina. La talasemia alfa es causada por la disminuci\u00f3n o ausencia de s\u00edntesis de cadenas de globina alfa, y la beta talasemia es causada por la s\u00edntesis reducida o ausente de las cadenas de globina beta. Los desequilibrios de cadenas de globina causan hem\u00f3lisis y deterioran la eritropoyesis.<br \/>\n<!--more--><br \/>\n<b>\u00cdndices hematol\u00f3gicos de la deficiencia de hierro y de las talasemias\u00a0Alfa y Beta\u00a0<\/b><\/p>\n<table style=\"border-collapse: collapse; width: 100%;\" border=\"1\">\n<tbody>\n<tr valign=\"TOP\">\n<td style=\"width: 32.363%;\" width=\"200\"><b>Prueba<\/b><\/td>\n<td style=\"width: 28.5959%; text-align: center;\" width=\"120\"><b>Deficiencia de hierro<\/b><\/td>\n<td style=\"width: 17.4658%; text-align: center;\" width=\"120\"><b>\u00a0Talasemia\u00a0<\/b><b>Beta<\/b><\/td>\n<td style=\"width: 21.5753%; text-align: center;\" width=\"120\"><b>Talasemia\u00a0<\/b><b>Alfa\u00a0<\/b><\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td style=\"width: 32.363%;\" width=\"200\">VCM (anormal si &lt;80 fl en adultos; &lt;70 fl en ni\u00f1os de 6 meses a 6 a\u00f1os de edad, y &lt;76 fl en ni\u00f1os de 7 a 12 a\u00f1os de edad)<\/td>\n<td style=\"width: 28.5959%; text-align: center;\" width=\"120\">Bajo<\/td>\n<td style=\"width: 17.4658%; text-align: center;\" width=\"120\">Bajo<\/td>\n<td style=\"width: 21.5753%; text-align: center;\" width=\"120\">Bajo<\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td style=\"width: 32.363%;\" width=\"200\">Amplitud de distribuci\u00f3n eritrocitaria<\/td>\n<td style=\"width: 28.5959%; text-align: center;\" width=\"120\">Alto<\/td>\n<td style=\"width: 17.4658%; text-align: center;\" width=\"120\">Normal;\u00a0ocasionalmente alta<\/td>\n<td style=\"width: 21.5753%; text-align: center;\" width=\"120\">Normal<\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td style=\"width: 32.363%;\" width=\"200\">Ferritina<\/td>\n<td style=\"width: 28.5959%; text-align: center;\" width=\"120\">Baja<\/td>\n<td style=\"width: 17.4658%; text-align: center;\" width=\"120\">Normal<\/td>\n<td style=\"width: 21.5753%; text-align: center;\" width=\"120\">Normal<\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td style=\"width: 32.363%;\" width=\"200\">\u00cdndice Mentzer para ni\u00f1os (VCM\/recuento de gl\u00f3bulos rojos)<\/td>\n<td style=\"width: 28.5959%; text-align: center;\" width=\"120\">&gt; 13<\/td>\n<td style=\"width: 17.4658%; text-align: center;\" width=\"120\">&lt; 13<\/td>\n<td style=\"width: 21.5753%; text-align: center;\" width=\"120\">&lt; 13<\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td style=\"width: 32.363%;\" width=\"200\">Electroforesis de Hb<\/td>\n<td style=\"width: 28.5959%; text-align: center;\" width=\"120\">Normal (puede haber reducida HbA2)<\/td>\n<td style=\"width: 17.4658%; text-align: center;\" width=\"120\">Aumentada HbA2, reducida HbA, y probablemente incrementada HbF<\/td>\n<td style=\"width: 21.5753%; text-align: center;\" width=\"120\">Reci\u00e9n nacidos: pueden tener HbH o Hb de Bart<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p>Hb = hemoglobina; HbF = hemoglobina fetal; VCM = volumen corpuscular medio.<\/p>\n<p>&nbsp;<\/p>\n<p><b>Bibliograf\u00eda:<\/b><\/p>\n<ol>\n<li>Martin A, Thompson AA. Thalassemias. Pediatr Clin North Am. 2013 Dec;60(6):1383-91.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/24237977\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Muncie HL Jr, Campbell J. Alpha and beta thalassemia. Am Fam Physician. 2009 Aug 15;80(4):339-44.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/19678601\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Piel FB, de Montalembert M, Das R, Kuo KHM, Taher AT, Musallam KM, Treadwell M, Fucharoen S, Angastiniotis M, Higgs D, Vichinsky E, Cappellini MD, De Franceschi L. Thalassaemia. Nat Rev Dis Primers. 2026 Jul 9;12(1):45. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/42426018\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado: Sep 14, 2015<br \/>\nActualizado: Oct 29, 2026.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Las talasemias son un grupo de trastornos hematol\u00f3gicos hereditarios causados por defectos en la s\u00edntesis de una o m\u00e1s de las cadenas de hemoglobina. La talasemia alfa es causada por la disminuci\u00f3n o ausencia de s\u00edntesis de cadenas de globina alfa, y la beta talasemia es causada por la s\u00edntesis reducida o ausente de las &#8230; <a title=\"Caracter\u00edsticas de las Talasemias\" class=\"read-more\" href=\"https:\/\/medicalcriteria.com\/web\/es\/hemth\/\" aria-label=\"Leer m\u00e1s sobre Caracter\u00edsticas de las Talasemias\">Leer m\u00e1s<\/a><\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"footnotes":""},"categories":[171],"tags":[864,863,862,861,860,41,859,858,857,856,855,865],"class_list":["post-2355","post","type-post","status-publish","format-standard","hentry","category-hematology","tag-alfa","tag-alpha","tag-beta","tag-cadenas","tag-chains","tag-features","tag-hemoglobin","tag-hemoglobina","tag-talasemia","tag-talasemias","tag-thalassemia","tag-thalassemias"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Caracter\u00edsticas de las Talasemias - MedicalCRITERIA.com<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/medicalcriteria.com\/web\/hemth\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"[:es]Caracter\u00edsticas de las Talasemias[:en]Features of the Thalassemias[:] - MedicalCRITERIA.com\" \/>\n<meta property=\"og:description\" content=\"Las talasemias son un grupo de trastornos hematol\u00f3gicos hereditarios causados por defectos en la s\u00edntesis de una o m\u00e1s de las cadenas de hemoglobina. 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