{"id":2386,"date":"2013-09-12T13:51:43","date_gmt":"2013-09-12T13:51:43","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/cryoglobulinemias\/"},"modified":"2025-05-13T20:27:52","modified_gmt":"2025-05-13T20:27:52","slug":"cryoglobulinemias","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/cryoglobulinemias\/","title":{"rendered":"Clasificaci\u00f3n y Caracter\u00edsticas Cl\u00ednico-Patol\u00f3gicas de las Diferentes Crioglobulinemias"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>Las crioglobulinemias generalmente se clasifican en tres grupos en funci\u00f3n de la composici\u00f3n de la inmunoglobulina: la crioglobulinemia tipo I est\u00e1 compuesta por un solo isotipo o subclase de inmunoglobulina. Tanto el tipo II y el tipo III, las crioglobulinas mixtas son complejos inmunes formados por IgG policlonales, autoant\u00edgenos, e IgM mono- o policlonal, respectivamente; las IgM son los autoanticuerpos correspondientes con la actividad del factor reumatoide (FR).<br \/>\n<!--more--><br \/>\n<strong>Clasificaci\u00f3n y caracter\u00edsticas cl\u00ednico-patol\u00f3gicas de las diferentes crioglobulinemias<\/strong><\/p>\n<table border=\"1\" width=\"100%\" cellspacing=\"0\" cellpadding=\"4\">\n<colgroup>\n<col width=\"64*\" \/>\n<col width=\"64*\" \/>\n<col width=\"64*\" \/>\n<col width=\"64*\" \/><\/colgroup>\n<tbody>\n<tr valign=\"TOP\">\n<td width=\"25%\"><strong>Crioglobulinas<\/strong><\/td>\n<td width=\"25%\"><strong>Composici\u00f3n<\/strong><\/td>\n<td width=\"25%\"><strong>Hallazgos patol\u00f3gicos<\/strong><\/td>\n<td width=\"25%\"><strong>Asociaciones cl\u00ednicas<\/strong><\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td width=\"25%\">Crioglobulinemia tipo I<\/td>\n<td width=\"25%\">Ig monoclonal, principalmente IgG, o IgM, o autoagregaci\u00f3n de IgA a trav\u00e9s de fragmento Fc de Ig<\/td>\n<td width=\"25%\">alteraciones histol\u00f3gicas de la enfermedad subyacente<\/td>\n<td width=\"25%\">-trastornos linfoproliferativos:<br \/>\nMM, WM, CLL, NHL de c\u00e9lulas B<\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td width=\"25%\">Crioglobulinemia mixta Tipo II<\/td>\n<td width=\"25%\">IgM monoclonal (o IgG, o IgA) con actividad de FR (con frecuencia idiotipo cruzado WA-mRF) e Ig policlonal (principalmente IgG)<\/td>\n<td width=\"25%\">-vasculitis leucocitocl\u00e1stica<br \/>\n-Expansi\u00f3n de linfocitos B con infiltrados tisulares<\/td>\n<td width=\"25%\">-infecciones (principalmente HCV, HBV, HIV)<br \/>\n-trastornos autoinmune\/ linfoproliferativos<br \/>\n&#8211; raramente \u00abesencial\u00bb<\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td width=\"25%\">Crioglobulinemia mixta tipo II -III<\/td>\n<td width=\"25%\">IgM FR oligoclonal o IgM mixto poli\/monoclonal (a menudo idiotipo cruzado WA- mRF)<\/td>\n<td width=\"25%\">-vasculitis leucocitocl\u00e1stica<br \/>\n-Expansi\u00f3n de linfocitos B con infiltrados tisulares<\/td>\n<td width=\"25%\">-infecciones (principalmente HCV, HBV, HIV)<br \/>\n-trastornos autoinmune\/ linfoproliferativos<br \/>\n&#8211; raramente \u00abesencial\u00bb<\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td width=\"25%\">Crioglobulinemia mixta tipo III<\/td>\n<td width=\"25%\">Ig policlonal mixta (todos los isotipos) con actividad de FR de un componente policlonal (por lo general IgM)<\/td>\n<td width=\"25%\">-vasculitis leucocitocl\u00e1stica<br \/>\n-Expansi\u00f3n de linfocitos B con infiltrados tisulares<\/td>\n<td width=\"25%\">-infecciones (principalmente HCV)<br \/>\n&#8211; m\u00e1s a menudo trastornos autoinmunes<br \/>\n&#8211; raramente \u00abesencial\u00bb<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p>Trastornos linfoproliferativos: MM (mieloma m\u00faltiple), WM (macroglobulinemia de Waldenstrom), LLC (leucemia linfoc\u00edtica cr\u00f3nica), LNH de c\u00e9lulas B (linfoma de Hodgkin de c\u00e9lulas B) ; Ig :inmunoglobulina; FR: factor reumatoide; VHB: Virus hepatitis B; VHC: virus hepatitis C<\/p>\n<p><strong>Criterios propuestos para la clasificaci\u00f3n de los pacientes con crioglobulinemia mixta (MC)<\/strong><\/p>\n<table border=\"1\" width=\"100%\" cellspacing=\"0\" cellpadding=\"4\">\n<colgroup>\n<col width=\"85*\" \/>\n<col width=\"85*\" \/>\n<col width=\"85*\" \/><\/colgroup>\n<tbody>\n<tr valign=\"TOP\">\n<td width=\"33%\"><strong>Criterios<\/strong><\/td>\n<td width=\"33%\"><strong>Mayor<\/strong><\/td>\n<td width=\"33%\"><strong>Menor<\/strong><\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td width=\"33%\">Serol\u00f3gica<\/td>\n<td width=\"33%\">Crioglobulinas mixta<br \/>\nC4 bajo<\/td>\n<td width=\"33%\">Factor reumatoide +<br \/>\nHCV +<br \/>\nHBV +<\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td width=\"33%\">Patol\u00f3gica<\/td>\n<td width=\"33%\">Vasculitis leucocitocl\u00e1stica<\/td>\n<td width=\"33%\">Infiltrado clonal de c\u00e9lulas B (h\u00edgado y\/o m\u00e9dula \u00f3sea)<\/td>\n<\/tr>\n<tr valign=\"TOP\">\n<td width=\"33%\">Cl\u00ednica<\/td>\n<td width=\"33%\">P\u00farpura<\/td>\n<td width=\"33%\">Hepatitis cr\u00f3nica<br \/>\nGlomerulonefritis membrano-proliferativa<br \/>\nNeuropat\u00eda perif\u00e9rica<br \/>\n\u00dalceras en piel<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p>S\u00edndrome de crioglobulinemia mixta \u00abDefinitiva\u00bb:<\/p>\n<ol style=\"list-style-type: lower-alpha;\">\n<li>Crioglobulinas mixtas en suero (\u00b1 C4 bajo) + p\u00farpura + vasculitis leucocitocl\u00e1stica.<\/li>\n<li>Crioglobulinas mixtas en suero (\u00b1 C4 bajo) + 2 s\u00edntomas cl\u00ednicos menores + 2 hallazgos serol\u00f3gicos\/patol\u00f3gicos menores.<\/li>\n<\/ol>\n<p>S\u00edndrome de crioglobulinemia mixta \u00abIncompleto\u00bb o \u00abposible\u00bb:<\/p>\n<ol style=\"list-style-type: lower-alpha;\">\n<li>Crioglobulinas mixtas o C4 bajo + 1 s\u00edntoma cl\u00ednico menor + 1 hallazgo serol\u00f3gico\u00b1patol\u00f3gico menor.<\/li>\n<li>P\u00farpura y\/o vasculitis leucocitocl\u00e1stica + 1 s\u00edntoma cl\u00ednico menor + 1 hallazgo serol\u00f3gico\u00b1patol\u00f3gico menor.<\/li>\n<li>Dos s\u00edntomas cl\u00ednicos menores + 2 hallazgos serol\u00f3gicos\u00b1patol\u00f3gicos menores.<\/li>\n<\/ol>\n<p>Crioglobulinemia mixta \u00abEsencial\u00bb o \u00absecundaria\u00bb:<br \/>\nAusencia o presencia de trastornos bien conocidos (infecciosas, inmunol\u00f3gicas, o neopl\u00e1sicas) en el momento del diagn\u00f3stico.<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li>Ferri C. Mixed cryoglobulinemia. Orphanet J Rare Dis. 2008 Sep 16;3:25. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/18796155\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medlne]<\/a><\/li>\n<li>Terrier B, Cacoub P. Cryoglobulinemia vasculitis: an update. Curr Opin Rheumatol. 2013 Jan;25(1):10-8. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/23196322\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Sep 12, 2013.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Las crioglobulinemias generalmente se clasifican en tres grupos en funci\u00f3n de la composici\u00f3n de la inmunoglobulina: la crioglobulinemia tipo I est\u00e1 compuesta por un solo isotipo o subclase de inmunoglobulina. Tanto el tipo II y el tipo III, las crioglobulinas mixtas son complejos inmunes formados por IgG policlonales, autoant\u00edgenos, e IgM mono- o policlonal, respectivamente; [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[289],"tags":[40,952,166,167,489,1046,1045,1044,1043,1042,1047],"class_list":["post-2386","post","type-post","status-publish","format-standard","hentry","category-immunology","tag-caracteristicas","tag-characteristics","tag-clasificacion","tag-classification","tag-clinico","tag-crioglobulinemias","tag-cryoglobulinemias","tag-diferenciales","tag-different","tag-pathological","tag-patologica"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Clasificaci\u00f3n y Caracter\u00edsticas Cl\u00ednico-Patol\u00f3gicas de las Diferentes Crioglobulinemias - MedicalCRITERIA.com<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/medicalcriteria.com\/web\/es\/cryoglobulinemias\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"[:es]Clasificaci\u00f3n y Caracter\u00edsticas Cl\u00ednico-Patol\u00f3gicas de las Diferentes Crioglobulinemias[:en]Classification and Clinico-Pathological Characteristics of Different Cryoglobulinemias[:] - MedicalCRITERIA.com\" \/>\n<meta property=\"og:description\" content=\"Las crioglobulinemias generalmente se clasifican en tres grupos en funci\u00f3n de la composici\u00f3n de la inmunoglobulina: la crioglobulinemia tipo I est\u00e1 compuesta por un solo isotipo o subclase de inmunoglobulina. 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