{"id":2425,"date":"2011-07-05T12:45:27","date_gmt":"2011-07-05T12:45:27","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/psynar\/"},"modified":"2025-05-13T20:28:55","modified_gmt":"2025-05-13T20:28:55","slug":"psynar","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/psynar\/","title":{"rendered":"Criterios Diagn\u00f3stico ICSD para Narcolepsia"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>La narcolepsia es un trastorno de expresi\u00f3n alterada de la vigilia y\u00a0del sue\u00f1o\u00a0REM (movimientos oculares\u00a0r\u00e1pidos).\u00a0Esto se manifiesta como somnolencia diurna excesiva y la expresi\u00f3n de cada uno de correlatos fisiol\u00f3gicos del sue\u00f1o REM, que incluyen la cataplej\u00eda y la par\u00e1lisis del sue\u00f1o (aton\u00eda del\u00a0sue\u00f1o REM que se introduce en la vigilia), mantenimiento deficiente de la aton\u00eda del sue\u00f1o REM (por ejemplo,\u00a0trastorno de la conducta del sue\u00f1o REM [TCSR]), e im\u00e1genes de sue\u00f1os que se introducen\u00a0en la vigilia (por ejemplo, alucinaciones hipnag\u00f3gicas e hipnop\u00f3mpicas).\u00a0La somnolencia excesiva suele comenzar en la segunda o tercera d\u00e9cada seguido por la expresi\u00f3n de s\u00edntomas auxiliares.<br \/>\n<!--more--><br \/>\n<strong>Criterios\u00a0<\/strong><strong>ICSD-1<\/strong>: criterios m\u00ednimos para el diagn\u00f3stico = B + C, o A + D + E + G.<br \/>\nA. El paciente se queja de la excesiva somnolencia diurna (ESD) o debilidad muscular s\u00fabita.<br \/>\nB.\u00a0Siestas o lapsos durante el d\u00eda de sue\u00f1o\u00a0recurrentes que se producen casi a diario durante al menos 3 meses.<br \/>\nC. P\u00e9rdida repentina del tono muscular\u00a0postural\u00a0bilateral que se produce en asociaci\u00f3n con emociones intensas (cataplej\u00eda).<br \/>\nD. Las caracter\u00edsticas asociadas incluyen:<\/p>\n<ol>\n<li>Par\u00e1lisis del sue\u00f1o<\/li>\n<li>Alucinaciones hipnag\u00f3gicas<\/li>\n<li>Comportamientos autom\u00e1ticos<\/li>\n<li>Episodios de sue\u00f1o interrumpidos importantes.<\/li>\n<\/ol>\n<p>E. La polisomnograf\u00eda (PSG) demuestra uno o m\u00e1s de los siguientes:<\/p>\n<ol>\n<li>Latencia del sue\u00f1o &lt;8 minutos<\/li>\n<li>Latencia del sue\u00f1o\u00a0REM &lt;20 minutos<\/li>\n<li>Prueba\u00a0de latencia\u00a0m\u00faltiple del sue\u00f1o (MSLT) que demuestra una latencia media de sue\u00f1o &lt;5 minutos<\/li>\n<li>Dos o m\u00e1s\u00a0per\u00edodos\u00a0al inicio del sue\u00f1o REM (SOREM).<\/li>\n<\/ol>\n<p>F. Tipificaci\u00f3n de HLA que\u00a0demuestra la positividad\u00a0DQB1*0602 o DR2.<br \/>\nG. Ausencia de trastornos mentales o m\u00e9dicos o mental que justifiquen los s\u00edntomas.<br \/>\nH. Otros trastornos del sue\u00f1o (por ejemplo, trastorno de movimientos peri\u00f3dicos de extremidades o el s\u00edndrome de apnea central del sue\u00f1o) pueden estar presentes, pero no son la principal causa de los s\u00edntomas.<\/p>\n<p><strong>Criterios\u00a0<\/strong><strong>ICSD-2:<\/strong><br \/>\nNarcolepsia con cataplejia:<\/p>\n<ul>\n<li>ESD diariamente por &gt; 3 meses<\/li>\n<li>Historia definida de cataplejia: episodios repentinos y transitorios de p\u00e9rdida del tono motor desencadenado por emociones<\/li>\n<li>El diagn\u00f3stico de la narcolepsia, siempre que sea posible, debe ser confirmado por PSG seguido por MSLT, este \u00faltimo muestra la latencia del sue\u00f1o &lt;\/= 8 minutos y &gt;\/= 2 SOREMs.\u00a0Por otra parte, los niveles de\u00a0hipocretina en\u00a0l\u00edquido cefalorraqu\u00eddeo &lt;\/= 110 pg\/mL<\/li>\n<li>Hipersomnia no explicada mejor por otra\u00a0enfermedad del\u00a0\u00a0sue\u00f1o, neurol\u00f3gica, mental, o\u00a0uso de sustancias\u00a0o medicamentos.<\/li>\n<\/ul>\n<p>Narcolepsia sin cataplej\u00eda:<\/p>\n<ul>\n<li>ESD\u00a0d\u00edariamente por &gt; 3 meses<\/li>\n<li>Cataplej\u00eda t\u00edpica no est\u00e1 presente<\/li>\n<li>El diagn\u00f3stico de narcolepsia DEBE ser confirmada por PSG seguido por MSLT, la \u00faltima muestra: latencia del sue\u00f1o &lt;\/=8 minutos y &gt;\/= 2 SOREMs<\/li>\n<li>Hipersomnia no explicada mejor por otra\u00a0enfermedad del\u00a0\u00a0sue\u00f1o, neurol\u00f3gica, mental, o\u00a0uso de sustancias\u00a0o medicamentos.<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li>Vignatelli L, Plazzi G, Bassein L, Barbato A, De Vincentiis A, Lugaresi E, D&#8217;Alessandro R; GIN-SEN. Gruppo Italiano Narcolessia-Studio Epidemiologico Nazionale. ICSD diagnostic criteria for narcolepsy: interobserver reliability. Intemational Classification of Sleep Disorders. Sleep. 2002 Mar 15;25(2):193-6. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/11902428\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Billiard M. Diagnosis of narcolepsy and idiopathic hypersomnia. An update based on the International classification of sleep disorders, 2nd edition. Sleep Med Rev. 2007 Oct;11(5):377-88. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/17646117\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Jul 5, 2011.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>La narcolepsia es un trastorno de expresi\u00f3n alterada de la vigilia y\u00a0del sue\u00f1o\u00a0REM (movimientos oculares\u00a0r\u00e1pidos).\u00a0Esto se manifiesta como somnolencia diurna excesiva y la expresi\u00f3n de cada uno de correlatos fisiol\u00f3gicos del sue\u00f1o REM, que incluyen la cataplej\u00eda y la par\u00e1lisis del sue\u00f1o (aton\u00eda del\u00a0sue\u00f1o REM que se introduce en la vigilia), mantenimiento deficiente de la [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[76],"tags":[16,15,14,13,1202,721,720],"class_list":["post-2425","post","type-post","status-publish","format-standard","hentry","category-psychiatry","tag-criteria","tag-criterios","tag-diagnostic","tag-diagnostico","tag-icsd","tag-narcolepsia","tag-narcolepsy"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - 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