{"id":2479,"date":"2009-03-24T11:32:43","date_gmt":"2009-03-24T11:32:43","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/neuromm\/"},"modified":"2025-05-14T19:09:29","modified_gmt":"2025-05-14T19:09:29","slug":"neuromm","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/neuromm\/","title":{"rendered":"Gu\u00eda para el Diagn\u00f3stico de Enfermedad de Moyamoya"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>La enfermedad de Moyamoya es una enfermedad cerebrovascular que predispone a los pacientes afectados a apoplej\u00eda en asociaci\u00f3n con estenosis progresivas de las arterias car\u00f3tidas internas intracraneales y sus ramas proximales.<!--more--><\/p>\n<p>1. Criterios Diagn\u00f3stico<\/p>\n<p>(1) La angiograf\u00eda cerebral es indispensable para el diagn\u00f3stico y deber\u00eda presentar al menos los siguientes hallazgos:<\/p>\n<blockquote><p>1) Estenosis u oclusi\u00f3n de la porci\u00f3n terminal de la arteria car\u00f3tida interna y\/o de la porci\u00f3n proximal de las arterias cerebral anterior y\/o media.<br \/>\n2) Red vascular anormal en la vecindad de las lesiones oclusivas o esten\u00f3ticas en la fase arterial.<br \/>\n3) Estos hallazgos deber\u00eda presentarse bilateralmente.<\/p><\/blockquote>\n<p>(2) Cuando las im\u00e1genes por Resonancia Magn\u00e9tica (RNM) y la angiograf\u00eda por Resonancia Magn\u00e9tica (MRA) claramente demuestran todos los hallazgos abajo descriptos, la angiograf\u00eda cerebral convencional no es obligatoria.<\/p>\n<blockquote><p>1) Estenosis u oclusi\u00f3n en la porci\u00f3n terminal de la\u00a0arteria car\u00f3tida interna y en la porci\u00f3n proximal de las arterias cerebral anterior y media en la MRA.<br \/>\n2) Una red vascular anormal en los n\u00facleos de la base en la MRA. Nota: Una red vascular anormal puede ser diagnosticada cuando se visualiza m\u00e1s de dos vac\u00edo de flujo aparente en un lado de los n\u00facleos de la base en la RNM.<br \/>\n3) 1) y 2) son encontrados bilateralmente. (Enviar a la Gu\u00eda de Diagn\u00f3stico por Im\u00e1genes por RNM y MRA.)<\/p><\/blockquote>\n<p>(3) Como la etiolog\u00eda de esta enfermedad es desconocida, la enfermedad cerebrovascular con las siguientes enfermedades o condiciones b\u00e1sicas deber\u00edan ser descartadas:<\/p>\n<blockquote><p>1) arterioesclerosis<br \/>\n2) enfermedad autoinmune<br \/>\n3) meningitis<br \/>\n4) neoplasias cerebrales<br \/>\n5) sindrome de Down<br \/>\n6) enfermedad de Recklinghausen<br \/>\n7) traumatismo encefalocraneano<br \/>\n8) irradiaci\u00f3n de la cabeza<br \/>\n9) otros<\/p><\/blockquote>\n<p>(4) Instructivo de hallazgos patol\u00f3gicos:<\/p>\n<blockquote><p>1) Engrosamiento de la \u00edntima y el resultado en en estenosis u oclusi\u00f3n de la luz son observado en y alrededor de la porci\u00f3n terminal de la arteria car\u00f3tida interna, usualmente bilateral. Dep\u00f3sitos lip\u00eddicos son ocasionalmente vistos en la proliferaci\u00f3n de la \u00edntima.<br \/>\n2) Arterias que constituyen el pol\u00edgono de Willis como la cerebral anterior y la media y las arterias comunicantes posterior a menudo muestran estenosis de varios grados u oclusi\u00f3n asociada con engrosamiento fibrocelular de la \u00edntima, un ondulamiento de la l\u00e1mina el\u00e1stica interna, y una atenuaci\u00f3n de la media.<br \/>\n3) Numerosos canales vasculares peque\u00f1os (ramas perforantes y anastomosis) son observados alrededor del pol\u00edgono de Willis.<br \/>\n4) Conglomerados reticulares de peque\u00f1os vasos son visualizados a menudo en la piamadre.<\/p><\/blockquote>\n<p>Diagn\u00f3stico<\/p>\n<p>En referencia a 1, mencionado m\u00e1s arriba, los criterios diagn\u00f3stico son clasificados como lo siguiente: Casos de autopsia que no han sido sometidos a angiograf\u00eda cerebral deber\u00edan ser investigados separadamente seg\u00fan se detalla en (4).<\/p>\n<blockquote><p>1. Caso definitivo<br \/>\nUno que cumpla cualquiera de (1) o (2), y (3). En ni\u00f1os, sin embargo, un caso que cumpla (3) y (1) 1) y 2) o (2) 1) y 2) en un lado y con estenosis marcada de la porci\u00f3n terminal de la arteria car\u00f3tida interna en el lado opuesto es tambi\u00e9n incluido.<br \/>\n2. Caso probable<br \/>\nUno que cumpla (1) 1) y 2) o (2) 1) y 2), y (3) (compromiso unilateral)<\/p><\/blockquote>\n<p>&nbsp;<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Bibliograf\u00eda<\/strong><\/p>\n<ol>\n<li>The Research Committee of Spontaneous Occlusion of the Circle of Willis (Moyamoya Disease) of the Ministry of Health and Welfare, Japan: Guidelines for diagnosis. Clin Neurol Neurosurg. 1997;99(suppl 2):S238\u2013S240.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/9409446\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<li>Scott RM, Smith ER. Moyamoya disease and moyamoya syndrome. N Engl J Med. 2009 Mar 19;360(12):1226-37.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/19297575\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Mar 24, 2009<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>La enfermedad de Moyamoya es una enfermedad cerebrovascular que predispone a los pacientes afectados a apoplej\u00eda en asociaci\u00f3n con estenosis progresivas de las arterias car\u00f3tidas internas intracraneales y sus ramas proximales.<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[2],"tags":[123,13,51,50,273,274,1453,1300],"class_list":["post-2479","post","type-post","status-publish","format-standard","hentry","category-neurology","tag-diagnosis","tag-diagnostico","tag-disease","tag-enfermedad","tag-guia","tag-guidelines","tag-moyamoya","tag-neurology"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - 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