{"id":2511,"date":"2009-03-08T12:10:41","date_gmt":"2009-03-08T12:10:41","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/neurotsc\/"},"modified":"2025-05-14T19:10:25","modified_gmt":"2025-05-14T19:10:25","slug":"neurotsc","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/neurotsc\/","title":{"rendered":"Criterios Diagn\u00f3stico para Complejo de Esclerosis Tuberosa (TSC)"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p><\/p>\n<div class=\"Section1\">\n<p style=\"font-weight: 400;\">Los criterios diagn\u00f3stico para el Complejo Esclerosis Tuberosa (TSC) fueron revisados en la Tuberous Sclerosis Complex Consensus Conference, Julio de 1998.<\/p>\n<p style=\"font-weight: 400;\"><strong>TSC Definitiva:<\/strong>\u00a0Dos criterios mayores o un criterio mayor m\u00e1s dos criterios menores<\/p>\n<p style=\"font-weight: 400;\"><strong>TSC Probable:<\/strong>\u00a0Un criterio mayor m\u00e1s un criterio menor<\/p>\n<p style=\"font-weight: 400;\"><strong>TSC Posible:<\/strong>\u00a0Un criterio mayor o dos criterios menores<\/p>\n<p><!--more--><\/p>\n<p style=\"font-weight: 400;\"><strong>Criterios Mayores<\/strong><\/p>\n<ul style=\"font-weight: 400;\">\n<li>Angiofibromas faciales o placas en la frente<\/li>\n<li>Fibromas no traum\u00e1ticos ungueales o periungueales<\/li>\n<li>M\u00e1culas hipomelan\u00f3ticas (tres o m\u00e1s)<\/li>\n<li>Placa de piel de zapa (nevus de tejido conectivo)<\/li>\n<li>Hamartomas nodulares retinales m\u00faltiples<\/li>\n<li>Tub\u00e9rculo cortical 1<\/li>\n<li>N\u00f3dulos subependimarios<\/li>\n<li>Astrocitoma de c\u00e9lulas gigantes subependimario<\/li>\n<li>Rabdomioma card\u00edaco, \u00fanico o m\u00faltiples<\/li>\n<li>Linfangiomiomatosis 2<\/li>\n<li>Angiomiolipoma renal 2<\/li>\n<\/ul>\n<p style=\"font-weight: 400;\"><strong>Criterios Menores<\/strong><\/p>\n<ul style=\"font-weight: 400;\">\n<li>Piqueteado m\u00faltiple del esmalte dental distribuido al azar<\/li>\n<li>P\u00f3lipos hamartomatosos rectales<\/li>\n<li>Quistes \u00f3seos<\/li>\n<li>L\u00edneas de migraci\u00f3n radial de la sustancia blanca cerebral 1,3<\/li>\n<li>Fibromas gingivales<\/li>\n<li>Hamartoma no renal<\/li>\n<li>Manchas acr\u00f3micas retinales<\/li>\n<li>Lesiones d\u00e9rmicas en \u00abConfetti\u00bb<\/li>\n<li>Quistes renales m\u00faltiples<\/li>\n<\/ul>\n<\/div>\n<p>&nbsp;<\/p>\n<p>1. La displasia cortical cerebral y las l\u00edneas de migraci\u00f3n de la sustancia blanca cerebral si ocurren conjuntamente son contados como uno en vez de dos caracter\u00edsticas de TSC.<br \/>\n2. Cuando ambos linfangiomiomatosis y angiomiolipomas renales est\u00e1n presentes, otro criterio de esclerosis tuberosa debe estar presente antes de realizar el diagn\u00f3stico de TSC.<br \/>\n3. Las l\u00edneas de migraci\u00f3n de la sustancia blanca y la displasia cortical focal son vistos a menudo en individuos con TSC; sin embargo, porque esas lesiones pueden ser vistas independientemente y son relativamente no espec\u00edficas, son consideradas como un criterio diagn\u00f3stico menor para TSC.<\/p>\n<div class=\"Section1\">\n<p>&nbsp;<\/p>\n<p style=\"font-weight: 400;\"><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol style=\"font-weight: 400;\">\n<li>Roach ES, DiMario FJ, Kandt RS, Northrup H. Tuberous Sclerosis Consensus Conference: recommendations for diagnostic evaluation. National Tuberous Sclerosis Association. J Child Neurol. 1999 Jun;14(6):401-7.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/10385849\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<li>Crino PB, Nathanson KL, Henske EP. The tuberous sclerosis complex. N Engl J Med. 2006 Sep 28;355(13):1345-56.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/17005952\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p style=\"font-weight: 400;\">Creado: Jul 05, 2005<\/p>\n<\/div>\n<p><\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Los criterios diagn\u00f3stico para el Complejo Esclerosis Tuberosa (TSC) fueron revisados en la Tuberous Sclerosis Complex Consensus Conference, Julio de 1998. TSC Definitiva:\u00a0Dos criterios mayores o un criterio mayor m\u00e1s dos criterios menores TSC Probable:\u00a0Un criterio mayor m\u00e1s un criterio menor TSC Posible:\u00a0Un criterio mayor o dos criterios menores<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[2],"tags":[95,16,15,14,13,94,1300,93,92,91,90],"class_list":["post-2511","post","type-post","status-publish","format-standard","hentry","category-neurology","tag-complex","tag-criteria","tag-criterios","tag-diagnostic","tag-diagnostico","tag-esclerosis","tag-neurology","tag-sclerosis","tag-tsc","tag-tuberosa","tag-tuberous"],"modified_by":"Guillermo Firman","_links":{"self":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/2511","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/comments?post=2511"}],"version-history":[{"count":3,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/2511\/revisions"}],"predecessor-version":[{"id":9143,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/2511\/revisions\/9143"}],"wp:attachment":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/media?parent=2511"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/categories?post=2511"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/tags?post=2511"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}