{"id":2560,"date":"2009-02-28T23:32:33","date_gmt":"2009-02-28T23:32:33","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/hemmastcla\/"},"modified":"2025-05-14T19:11:32","modified_gmt":"2025-05-14T19:11:32","slug":"hemmastcla","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/hemmastcla\/","title":{"rendered":"Criterios Diagn\u00f3stico para Mastocitosis Sist\u00e9mica (MS)"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>Si al menos presenta 1 mayor y 1 menor, o al menos 3 criterios menores, son encontrados, el diagn\u00f3stico de Mastocitosis Sist\u00e9mica (MS) puede ser establecido.<br \/>\n<!--more--><\/p>\n<p style=\"font-weight: 400;\"><strong>Criterio Mayor:<\/strong>\u00a0Infiltrados densos multifocales de mastocitos en m\u00e9dula \u00f3sea u otro \u00f3rgano(s) extracut\u00e1neo (&gt;15 mastocitos en aglomerados)<\/p>\n<p style=\"font-weight: 400;\"><strong>Criterios Menores:<\/strong><\/p>\n<ol>\n<li style=\"font-weight: 400;\">Mastocitos en m\u00e9dula \u00f3sea u otro \u00f3rgano(s) extracut\u00e1neo mostrando una morfolog\u00eda anormal (&gt; 25%)<\/li>\n<li style=\"font-weight: 400;\">Mutaci\u00f3n del protooncog\u00e9n c-kit en el cod\u00f3n 816 en \u00f3rgano(s) extracut\u00e1neos (Mutaciones activantes en el cod\u00f3n 816; en la mayor\u00eda de los casos, c-kit D816V)<\/li>\n<li style=\"font-weight: 400;\">Mastocitos en m\u00e9dula \u00f3sea que expresan CD2 y\/o CD25<\/li>\n<li style=\"font-weight: 400;\">Triptasa s\u00e9rica total &gt; 20 ng\/mL (Esto no es v\u00e1lido para pacientes que presentan asociada a otras enfermedades hematol\u00f3gicas clonales con c\u00e9lulas no-mastocitos)<\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p style=\"font-weight: 400;\"><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li>Akin C, Metcalfe DD. Systemic mastocytosis. Annu Rev Med. 2004;55:419-32.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/14746529\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>O&#8217;Brien S, Tefferi A, Valent P. Chronic myelogenous leukemia and myeloproliferative disease. Hematology (Am Soc Hematol Educ Program). 2004;:146-62.\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/15561681\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado: Jun 21, 2005<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Si al menos presenta 1 mayor y 1 menor, o al menos 3 criterios menores, son encontrados, el diagn\u00f3stico de Mastocitosis Sist\u00e9mica (MS) puede ser establecido.<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[171],"tags":[16,15,14,13,1381,1716,1715,1714,1088],"class_list":["post-2560","post","type-post","status-publish","format-standard","hentry","category-hematology","tag-criteria","tag-criterios","tag-diagnostic","tag-diagnostico","tag-hematology","tag-mastocitosis","tag-mastocytosis","tag-sm","tag-systemic"],"modified_by":"Guillermo Firman","_links":{"self":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/2560","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/comments?post=2560"}],"version-history":[{"count":4,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/2560\/revisions"}],"predecessor-version":[{"id":9375,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/2560\/revisions\/9375"}],"wp:attachment":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/media?parent=2560"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/categories?post=2560"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/tags?post=2560"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}