{"id":8165,"date":"2020-12-10T20:30:56","date_gmt":"2020-12-10T20:30:56","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/?p=8165"},"modified":"2026-01-07T18:49:42","modified_gmt":"2026-01-07T18:49:42","slug":"myelodysplasia","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/myelodysplasia\/","title":{"rendered":"Criterios Diagn\u00f3stico para Neoplasias Mieloides con Mielodisplasia"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>Los s\u00edndromes mielodispl\u00e1sicos (SMD) son neoplasias mieloides que se caracterizan por la proliferaci\u00f3n clonal de c\u00e9lulas madre hematopoy\u00e9ticas, anomal\u00edas gen\u00e9ticas recurrentes, mielodisplasia, hematopoyesis ineficaz, citopenia de sangre perif\u00e9rica y un alto riesgo de evoluci\u00f3n a leucemia mieloide aguda (LMA). <!--more--><\/p>\n<p><strong>Criterios de diagn\u00f3stico para neoplasias mieloides con mielodisplasia y condiciones precursoras de s\u00edndromes mielodispl\u00e1sicos (SMD)<\/strong><\/p>\n<table style=\"border-collapse: collapse; width: 100%;\" border=\"1\">\n<tbody>\n<tr>\n<td style=\"width: 23.4589%;\"><strong>Enfermedad<\/strong><\/td>\n<td style=\"width: 76.5411%;\"><strong>Criterios <\/strong><strong>Diagn\u00f3stico<\/strong><\/td>\n<\/tr>\n<tr>\n<td style=\"width: 100%;\" colspan=\"2\"><strong>Neoplasias mieloides con mielodisplasia<\/strong><\/td>\n<\/tr>\n<tr>\n<td style=\"width: 23.4589%;\">SMD<\/td>\n<td style=\"width: 76.5411%;\">Citopenia persistente en uno o m\u00e1s linajes de c\u00e9lulas de sangre perif\u00e9rica y displasia morfol\u00f3gica (\u226510% de c\u00e9lulas displ\u00e1sicas) en uno o m\u00e1s linajes de c\u00e9lulas de la m\u00e9dula \u00f3sea. Sobre la base de anomal\u00edas morfol\u00f3gicas y citogen\u00e9ticas, los SMD se clasifican en los siguientes subtipos:<br \/>\nSMD con displasia de linaje \u00fanico<br \/>\nSMD con displasia multilinaje<br \/>\nSMD con sideroblastos en anillo y displasia de linaje \u00fanico o displasia de linaje m\u00faltiple<br \/>\nSMD con del(5q) aislado<br \/>\nSMD con exceso de blastos tipo 1 o tipo 2<br \/>\nSMD, no clasificable<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 23.4589%;\">Neoplasias mielodispl\u00e1sicas &#8211; mieloproliferativas<\/td>\n<td style=\"width: 76.5411%;\">Neoplasias mieloides con caracter\u00edsticas cl\u00ednicas, de laboratorio y morfol\u00f3gicas que se superponen a las de los SMD y las neoplasias mieloproliferativas. Las neoplasias mielodispl\u00e1sicas-mieloproliferativas se dividen en los siguientes subtipos:<br \/>\nLeucemia mielomonoc\u00edtica cr\u00f3nica<br \/>\nLeucemia mieloide cr\u00f3nica at\u00edpica negativa para BCR-ABL1<br \/>\nNeoplasia mielodispl\u00e1sica-mieloproliferativa con sideroblastos en anillo y trombocitosis<br \/>\nLeucemia mielomonoc\u00edtica juvenil<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 23.4589%;\">Neoplasias mieloides relacionadas con la terapia<\/td>\n<td style=\"width: 76.5411%;\">SMD, neoplasias mielodispl\u00e1sicas mieloproliferativas y leucemia mieloide aguda que se presentan como complicaciones tard\u00edas de la quimioterapia o la radioterapia<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 100%;\" colspan=\"2\"><strong>Condiciones precursoras de SMD<\/strong><\/td>\n<\/tr>\n<tr>\n<td style=\"width: 23.4589%;\">Hematopoyesis Clonal de Potencial Indeterminado (CHIP)<\/td>\n<td style=\"width: 76.5411%;\">Recuento normal de c\u00e9lulas de sangre perif\u00e9rica con una mutaci\u00f3n som\u00e1tica, con una frecuencia de alelos variante de al menos 2%, en un gen que muta de forma recurrente en las neoplasias mieloides\u2021<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 23.4589%;\">Citopenia Clonal de Significado Indeterminado (CCUS)<\/td>\n<td style=\"width: 76.5411%;\">Citopenia inexplicable en uno o m\u00e1s linajes de c\u00e9lulas de sangre perif\u00e9rica; una mutaci\u00f3n som\u00e1tica, con una frecuencia de alelos variante de al menos el 20%, en uno o m\u00e1s genes que mutan de forma recurrente en neoplasias mieloides; y criterios insuficientes de la OMS para un diagn\u00f3stico de SMD, esencialmente debido a la falta de displasia manifiesta (&lt;10% de c\u00e9lulas displ\u00e1sicas en cualquier linaje de c\u00e9lulas de la m\u00e9dula \u00f3sea), exceso de blastos y anomal\u00edas cromos\u00f3micas que definen SMD\u00a7<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p>\u2021 Las personas con CHIP pueden tener valores aumentados para el ancho de distribuci\u00f3n de gl\u00f3bulos rojos.<br \/>\n\u00a7 Aunque inicialmente se sugiri\u00f3 una frecuencia de alelos variante de al menos 2% para el diagn\u00f3stico de CCUS, la evidencia disponible indica que se debe usar un punto de corte m\u00e1s alto (20%) para identificar la clonalidad cl\u00ednicamente significativa.<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li>Cazzola M. Myelodysplastic Syndromes. N Engl J Med. 2020 Oct 1;383(14):1358-1374. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/32997910\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Shreve J, Nazha A. Novel Prognostic Models for Myelodysplastic Syndromes. Hematol Oncol Clin North Am. 2020 Apr;34(2):369-378. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/32089216\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Nov 26, 2020.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>Los s\u00edndromes mielodispl\u00e1sicos (SMD) son neoplasias mieloides que se caracterizan por la proliferaci\u00f3n clonal de c\u00e9lulas madre hematopoy\u00e9ticas, anomal\u00edas gen\u00e9ticas recurrentes, mielodisplasia, hematopoyesis ineficaz, citopenia de sangre perif\u00e9rica y un alto riesgo de evoluci\u00f3n a leucemia mieloide aguda (LMA).<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[171],"tags":[16,15,14,13,2289,2288,2286,2284,2287,2285],"class_list":["post-8165","post","type-post","status-publish","format-standard","hentry","category-hematology","tag-criteria","tag-criterios","tag-diagnostic","tag-diagnostico","tag-mielodisplasia","tag-mieloides","tag-myelodysplasia","tag-myeloid","tag-neoplasias","tag-neoplasms"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - 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