{"id":8381,"date":"2021-01-29T21:07:24","date_gmt":"2021-01-29T21:07:24","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/?p=8381"},"modified":"2026-01-06T20:45:38","modified_gmt":"2026-01-06T20:45:38","slug":"igg4-sc","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/","title":{"rendered":"Criterios de Diagn\u00f3stico Cl\u00ednico de Colangitis Esclerosante Relacionada con IgG4 (CE-IgG4)"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>La colangitis esclerosante (CE) se define como una condici\u00f3n con estenosis progresiva y destrucci\u00f3n de los conductos biliares debido a inflamaci\u00f3n difusa y fibrosis. Actualmente incluye tres categor\u00edas: colangitis esclerosante primaria (CEP), colangitis secundaria y colangitis esclerosante relacionada con IgG4 (CE-IgG4). Las categor\u00edas de CE comparten caracter\u00edsticas cl\u00ednicas similares, como la colestasis. Los pacientes con CE se presentan con s\u00edntomas colest\u00e1sicos, que incluyen ictericia y prurito, y los an\u00e1lisis de sangre revelan elevaci\u00f3n de las enzimas colest\u00e1sicas.<!--more--><\/p>\n<p><strong>Criterios de diagn\u00f3stico cl\u00ednico de colangitis esclerosante relacionada con IgG4<\/strong><\/p>\n<p><strong>Elementos de diagn\u00f3stico<\/strong><\/p>\n<ol>\n<li>Las im\u00e1genes del tracto biliar revelan un estrechamiento difuso o segmentario del conducto biliar intrahep\u00e1tico y\/o extrahep\u00e1tico, asociado con un engrosamiento de la pared del conducto biliar<\/li>\n<li>El examen hematol\u00f3gico muestra una concentraci\u00f3n s\u00e9rica elevada de IgG4 (\u2265135 mg\/dL)<\/li>\n<li>Coexistencia de <a href=\"https:\/\/medicalcriteria.com\/web\/es\/autoimmune-pancreatitis\/\" target=\"_blank\" rel=\"noopener noreferrer\">pancreatitis autoinmune<\/a>, dacrioadenitis\/sialadenitis relacionada con IgG4 o fibrosis retroperitoneal relacionada con IgG4<\/li>\n<li>El examen histopatol\u00f3gico muestra:<\/li>\n<\/ol>\n<ol>\n<li style=\"list-style-type: none;\">\n<ol style=\"list-style-type: lower-alpha;\">\n<li>Infiltraci\u00f3n y fibrosis marcada de linfocitos y plasmocitos<\/li>\n<li>Infiltraci\u00f3n de c\u00e9lulas plasm\u00e1ticas positivas para IgG4 (&gt; 10 c\u00e9lulas por campo de alta potencia)<\/li>\n<li>Fibrosis estoriforme<\/li>\n<li>Flebitis obliterante<\/li>\n<\/ol>\n<\/li>\n<\/ol>\n<p><strong>Opcional:<\/strong> efectividad de la terapia con esteroides<\/p>\n<p><strong>Diagn\u00f3stico<\/strong><\/p>\n<ul>\n<li>Diagn\u00f3stico definitivo: (1) + (3), o (1) + (2) + (4) (a + b, o a + b + c, o a + b + d)<\/li>\n<li>Diagn\u00f3stico probable: (1) + (2) + elemento opcional<\/li>\n<li>Diagn\u00f3stico posible: (1) + (2)<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li>Tanaka A. IgG4-Related Sclerosing Cholangitis and Primary Sclerosing Cholangitis. Gut Liver. 2019 May 15;13(3):300-307. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/30205418\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Tanaka A. Immunoglobulin G4-related sclerosing cholangitis. J Dig Dis. 2019 Jul;20(7):357-362. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/31112324\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Naitoh I, Yoshida M, Nakazawa T. Endoscopic diagnosis of immunoglobulin G4-related sclerosing cholangitis. Dig Endosc. 2025 Aug;37(8):824-833. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/40256978\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado: Ene 27, 2021.<br \/>\nActualizado Ene 06, 2026.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>La colangitis esclerosante (CE) se define como una condici\u00f3n con estenosis progresiva y destrucci\u00f3n de los conductos biliares debido a inflamaci\u00f3n difusa y fibrosis. Actualmente incluye tres categor\u00edas: colangitis esclerosante primaria (CEP), colangitis secundaria y colangitis esclerosante relacionada con IgG4 (CE-IgG4). Las categor\u00edas de CE comparten caracter\u00edsticas cl\u00ednicas similares, como la colestasis. Los pacientes con [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[53],"tags":[376,490,489,375,16,15,14,13,660,2308,2309,1563,662],"class_list":["post-8381","post","type-post","status-publish","format-standard","hentry","category-gastroenterology","tag-cholangitis","tag-clinical","tag-clinico","tag-colangitis","tag-criteria","tag-criterios","tag-diagnostic","tag-diagnostico","tag-esclerosante","tag-igg4","tag-relacionada","tag-related","tag-sclerosing"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Criterios de Diagn\u00f3stico Cl\u00ednico de Colangitis Esclerosante Relacionada con IgG4 (CE-IgG4) - MedicalCRITERIA.com<\/title>\n<meta name=\"description\" content=\"La colangitis esclerosante (CE) se define como una condici\u00f3n con estenosis progresiva y destrucci\u00f3n de los conductos biliares debido a inflamaci\u00f3n difusa y fibrosis. Actualmente incluye tres categor\u00edas: colangitis esclerosante primaria (CEP), colangitis secundaria y colangitis esclerosante relacionada con IgG4 (CE-IgG4). Las categor\u00edas de CE comparten caracter\u00edsticas cl\u00ednicas similares, como la colestasis. Los pacientes con CE se presentan con s\u00edntomas colest\u00e1sicos, que incluyen ictericia y prurito, y los an\u00e1lisis de sangre revelan elevaci\u00f3n de las enzimas colest\u00e1sicas.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"[:es]Criterios de Diagn\u00f3stico Cl\u00ednico de Colangitis Esclerosante Relacionada con IgG4 (CE-IgG4)[:en]Clinical Diagnostic Criteria of IgG4-Related Sclerosing Cholangitis (IgG4-SC)[:] - MedicalCRITERIA.com\" \/>\n<meta property=\"og:description\" content=\"La colangitis esclerosante (CE) se define como una condici\u00f3n con estenosis progresiva y destrucci\u00f3n de los conductos biliares debido a inflamaci\u00f3n difusa y fibrosis. Actualmente incluye tres categor\u00edas: colangitis esclerosante primaria (CEP), colangitis secundaria y colangitis esclerosante relacionada con IgG4 (CE-IgG4). Las categor\u00edas de CE comparten caracter\u00edsticas cl\u00ednicas similares, como la colestasis. Los pacientes con CE se presentan con s\u00edntomas colest\u00e1sicos, que incluyen ictericia y prurito, y los an\u00e1lisis de sangre revelan elevaci\u00f3n de las enzimas colest\u00e1sicas.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/\" \/>\n<meta property=\"og:site_name\" content=\"MedicalCRITERIA.com\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/medicalcriteria\/\" \/>\n<meta property=\"article:published_time\" content=\"2021-01-29T21:07:24+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2026-01-06T20:45:38+00:00\" \/>\n<meta name=\"author\" content=\"Guillermo Firman\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Escrito por\" \/>\n\t<meta name=\"twitter:data1\" content=\"Guillermo Firman\" \/>\n\t<meta name=\"twitter:label2\" content=\"Tiempo de lectura\" \/>\n\t<meta name=\"twitter:data2\" content=\"1 minuto\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/es\\\/igg4-sc\\\/#article\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/es\\\/igg4-sc\\\/\"},\"author\":{\"name\":\"Guillermo Firman\",\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/#\\\/schema\\\/person\\\/ead6734a2f20659131388ba822c7078c\"},\"headline\":\"Criterios de Diagn\u00f3stico Cl\u00ednico de Colangitis Esclerosante Relacionada con IgG4 (CE-IgG4)\",\"datePublished\":\"2021-01-29T21:07:24+00:00\",\"dateModified\":\"2026-01-06T20:45:38+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/es\\\/igg4-sc\\\/\"},\"wordCount\":547,\"publisher\":{\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/#organization\"},\"keywords\":[\"Cholangitis\",\"Clinical\",\"clinico\",\"colangitis\",\"Criteria\",\"criterios\",\"Diagnostic\",\"diagnostico\",\"esclerosante\",\"IgG4\",\"Relacionada\",\"Related\",\"Sclerosing\"],\"articleSection\":[\"Gastroenterology\"],\"inLanguage\":\"es\"},{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/es\\\/igg4-sc\\\/\",\"url\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/es\\\/igg4-sc\\\/\",\"name\":\"[:es]Criterios de Diagn\u00f3stico Cl\u00ednico de Colangitis Esclerosante Relacionada con IgG4 (CE-IgG4)[:en]Clinical Diagnostic Criteria of IgG4-Related Sclerosing Cholangitis (IgG4-SC)[:] - MedicalCRITERIA.com\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/#website\"},\"datePublished\":\"2021-01-29T21:07:24+00:00\",\"dateModified\":\"2026-01-06T20:45:38+00:00\",\"description\":\"La colangitis esclerosante (CE) se define como una condici\u00f3n con estenosis progresiva y destrucci\u00f3n de los conductos biliares debido a inflamaci\u00f3n difusa y fibrosis. 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Actualmente incluye tres categor\u00edas: colangitis esclerosante primaria (CEP), colangitis secundaria y colangitis esclerosante relacionada con IgG4 (CE-IgG4). Las categor\u00edas de CE comparten caracter\u00edsticas cl\u00ednicas similares, como la colestasis. 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Los pacientes con CE se presentan con s\u00edntomas colest\u00e1sicos, que incluyen ictericia y prurito, y los an\u00e1lisis de sangre revelan elevaci\u00f3n de las enzimas colest\u00e1sicas.","og_url":"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/","og_site_name":"MedicalCRITERIA.com","article_publisher":"https:\/\/www.facebook.com\/medicalcriteria\/","article_published_time":"2021-01-29T21:07:24+00:00","article_modified_time":"2026-01-06T20:45:38+00:00","author":"Guillermo Firman","twitter_card":"summary_large_image","twitter_misc":{"Escrito por":"Guillermo Firman","Tiempo de lectura":"1 minuto"},"schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"Article","@id":"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/#article","isPartOf":{"@id":"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/"},"author":{"name":"Guillermo Firman","@id":"https:\/\/medicalcriteria.com\/web\/#\/schema\/person\/ead6734a2f20659131388ba822c7078c"},"headline":"Criterios de Diagn\u00f3stico Cl\u00ednico de Colangitis Esclerosante Relacionada con IgG4 (CE-IgG4)","datePublished":"2021-01-29T21:07:24+00:00","dateModified":"2026-01-06T20:45:38+00:00","mainEntityOfPage":{"@id":"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/"},"wordCount":547,"publisher":{"@id":"https:\/\/medicalcriteria.com\/web\/#organization"},"keywords":["Cholangitis","Clinical","clinico","colangitis","Criteria","criterios","Diagnostic","diagnostico","esclerosante","IgG4","Relacionada","Related","Sclerosing"],"articleSection":["Gastroenterology"],"inLanguage":"es"},{"@type":"WebPage","@id":"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/","url":"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/","name":"[:es]Criterios de Diagn\u00f3stico Cl\u00ednico de Colangitis Esclerosante Relacionada con IgG4 (CE-IgG4)[:en]Clinical Diagnostic Criteria of IgG4-Related Sclerosing Cholangitis (IgG4-SC)[:] - MedicalCRITERIA.com","isPartOf":{"@id":"https:\/\/medicalcriteria.com\/web\/#website"},"datePublished":"2021-01-29T21:07:24+00:00","dateModified":"2026-01-06T20:45:38+00:00","description":"La colangitis esclerosante (CE) se define como una condici\u00f3n con estenosis progresiva y destrucci\u00f3n de los conductos biliares debido a inflamaci\u00f3n difusa y fibrosis. Actualmente incluye tres categor\u00edas: colangitis esclerosante primaria (CEP), colangitis secundaria y colangitis esclerosante relacionada con IgG4 (CE-IgG4). Las categor\u00edas de CE comparten caracter\u00edsticas cl\u00ednicas similares, como la colestasis. Los pacientes con CE se presentan con s\u00edntomas colest\u00e1sicos, que incluyen ictericia y prurito, y los an\u00e1lisis de sangre revelan elevaci\u00f3n de las enzimas colest\u00e1sicas.","breadcrumb":{"@id":"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/#breadcrumb"},"inLanguage":"es","potentialAction":[{"@type":"ReadAction","target":["https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/"]}]},{"@type":"BreadcrumbList","@id":"https:\/\/medicalcriteria.com\/web\/es\/igg4-sc\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Portada","item":"https:\/\/medicalcriteria.com\/web\/"},{"@type":"ListItem","position":2,"name":"Criterios de Diagn\u00f3stico Cl\u00ednico de Colangitis Esclerosante Relacionada con IgG4 (CE-IgG4)"}]},{"@type":"WebSite","@id":"https:\/\/medicalcriteria.com\/web\/#website","url":"https:\/\/medicalcriteria.com\/web\/","name":"MedicalCRITERIA.com","description":"Unifying Concepts","publisher":{"@id":"https:\/\/medicalcriteria.com\/web\/#organization"},"potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/medicalcriteria.com\/web\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"es"},{"@type":"Organization","@id":"https:\/\/medicalcriteria.com\/web\/#organization","name":"MedicalCRITERIA.com","alternateName":"Criterios M\u00e9dicos","url":"https:\/\/medicalcriteria.com\/web\/","logo":{"@type":"ImageObject","inLanguage":"es","@id":"https:\/\/medicalcriteria.com\/web\/#\/schema\/logo\/image\/","url":"https:\/\/medicalcriteria.com\/web\/wp-content\/uploads\/2025\/03\/cropped-mc_1024x500.png","contentUrl":"https:\/\/medicalcriteria.com\/web\/wp-content\/uploads\/2025\/03\/cropped-mc_1024x500.png","width":600,"height":257,"caption":"MedicalCRITERIA.com"},"image":{"@id":"https:\/\/medicalcriteria.com\/web\/#\/schema\/logo\/image\/"},"sameAs":["https:\/\/www.facebook.com\/medicalcriteria\/"]},{"@type":"Person","@id":"https:\/\/medicalcriteria.com\/web\/#\/schema\/person\/ead6734a2f20659131388ba822c7078c","name":"Guillermo Firman","image":{"@type":"ImageObject","inLanguage":"es","@id":"https:\/\/secure.gravatar.com\/avatar\/24f0f68ba780b5b240680962755c6f75e6116e6667394a46e38b7b8fd0a62e9f?s=96&d=mm&r=g","url":"https:\/\/secure.gravatar.com\/avatar\/24f0f68ba780b5b240680962755c6f75e6116e6667394a46e38b7b8fd0a62e9f?s=96&d=mm&r=g","contentUrl":"https:\/\/secure.gravatar.com\/avatar\/24f0f68ba780b5b240680962755c6f75e6116e6667394a46e38b7b8fd0a62e9f?s=96&d=mm&r=g","caption":"Guillermo Firman"},"sameAs":["http:\/\/MedicalCRITERIA.com"]}]}},"modified_by":"Guillermo Firman","_links":{"self":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/8381","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/comments?post=8381"}],"version-history":[{"count":8,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/8381\/revisions"}],"predecessor-version":[{"id":10566,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/8381\/revisions\/10566"}],"wp:attachment":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/media?parent=8381"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/categories?post=8381"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/tags?post=8381"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}