{"id":9,"date":"2009-02-13T18:50:10","date_gmt":"2009-02-13T18:50:10","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/neuroals\/"},"modified":"2025-05-14T21:05:59","modified_gmt":"2025-05-14T21:05:59","slug":"neuroals","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/neuroals\/","title":{"rendered":"Criterios El Escorial para el Diagn\u00f3stico de Esclerosis Lateral Amiotr\u00f3fica (ELA)"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p><\/p>\n<p style=\"font-weight: 400;\">El Comit\u00e9 de la World Federation of Neurology, en 1994 present\u00f3 los Criterios de El Escorial, usados hasta la fecha como gu\u00edas diagn\u00f3sticas. Para realizar el diagn\u00f3stico de Esclerosis Lateral Amiotr\u00f3fica (ELA) se requiere:<!--more--><\/p>\n<p>A- Presencia de:<br \/>\n(A:1) Evidencia de degeneraci\u00f3n del tipo de neurona motora inferior (NMI), por examen cl\u00ednico, electrofisiol\u00f3gico o neuropatol\u00f3gico.<br \/>\n(A:2) Evidencia de degeneraci\u00f3n de neurona motora superior (NMS) por examen cl\u00ednico y<br \/>\n(A:3) Diseminaci\u00f3n progresivo de los s\u00edntomas o signos dentro de una regi\u00f3n o de otras regiones, determinados por medio de la historia cl\u00ednica o exploraci\u00f3n f\u00edsica, junto con<\/p>\n<p>B- Ausencia de:<br \/>\n(B:1) Evidencia electrofisiol\u00f3gica o patol\u00f3gica de otra enfermedad o proceso que pueda explicar los signos de degeneraci\u00f3n de neurona motora superior o inferior, y<br \/>\n(B:2) Evidencia de neuroimagen de otro proceso o enfermedad, que pueda explicar los signos cl\u00ednicos y electrofisiol\u00f3gicos explicados.<\/p>\n<p style=\"font-weight: 400;\">El diagn\u00f3stico cl\u00ednico de ELA, sin confirmaci\u00f3n patol\u00f3gica,<\/p>\n<p style=\"font-weight: 400;\"><strong>Categor\u00edas diagn\u00f3sticas<\/strong><\/p>\n<ol>\n<li style=\"font-weight: 400;\"><strong>ELA Definitiva:<\/strong>Evidencia cl\u00ednica de signos de NMS y de NMI en 3 regiones.*<\/li>\n<li style=\"font-weight: 400;\"><strong>ELA probable:<\/strong>Evidencia cl\u00ednica de signos de NMS y de NMI en al menos 2 regiones, con los signos de NMS predominando sobre los de NMI.<\/li>\n<li style=\"font-weight: 400;\"><strong>ELA posible:<\/strong>Evidencia cl\u00ednica de signos de NMS y de NMI en una regi\u00f3n; o los signos de NMS est\u00e1n solamente presentes en una regi\u00f3n, y los signos de NMI est\u00e1n definidos por criterios de\u00a0electromiograf\u00eda\u00a0(EMG) en al menos 2 extremidades; con la apropiada aplicaci\u00f3n de protocolos de neuroimagen y laboratorio para excluir otras causas.<\/li>\n<li style=\"font-weight: 400;\"><strong>Sospecha de ELA:<\/strong>Signos puros de NMI en 2 \u00f3 3 regiones (p. Ej., atrofia muscular progresiva y otros s\u00edndromes motores).<\/li>\n<\/ol>\n<p style=\"font-weight: 400;\">* regi\u00f3n: bulbo raqu\u00eddeo, m\u00e9dula cervical, m\u00e9dula dorsal, m\u00e9dula lumbosacra.<\/p>\n<p style=\"font-weight: 400;\">NMS: neurona motora superior. NMI: neurona motora inferior.\u00a0EMG: electromiograf\u00eda.<\/p>\n<p>&nbsp;<\/p>\n<p style=\"font-weight: 400;\"><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol style=\"font-weight: 400;\">\n<li>Brooks BR. El Escorial World Federation of Neurology criteria for the diagnosis of amyotrophic lateral sclerosis. Subcommittee on Motor Neuron Diseases\/Amyotrophic Lateral Sclerosis of the World Federation of Neurology Research Group on Neuromuscular Diseases and the El Escorial \u00abClinical limits of amyotrophic lateral sclerosis\u00bb workshop contributors. J Neurol Sci. 1994 Jul;124 Suppl:96-107. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/7807156\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<li>Mitsumoto H. Diagnosis and progression of ALS. Neurology 1997; 48(S4):2S-8S.<\/li>\n<li>Ross MA, Miller RG, Berchert L, Parry G, Barohn RJ, Armon C, Bryan WW, Petajan J, Stromatt S, Goodpasture J, McGuire D. Toward earlier diagnosis of amyotrophic lateral sclerosis: revised criteria. rhCNTF ALS Study Group. Neurology. 1998 Mar;50(3):768-72. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/9521272\/\" target=\"_blank\" rel=\"noopener noreferrer\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p style=\"font-weight: 400;\">Creado: Jul 13, 2008<\/p>\n<p><\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>El Comit\u00e9 de la World Federation of Neurology, en 1994 present\u00f3 los Criterios de El Escorial, usados hasta la fecha como gu\u00edas diagn\u00f3sticas. Para realizar el diagn\u00f3stico de Esclerosis Lateral Amiotr\u00f3fica (ELA) se requiere:<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[2],"tags":[1952,1951,1950,16,15,123,13,1949,1948,94,1947,1946,1300,93],"class_list":["post-9","post","type-post","status-publish","format-standard","hentry","category-neurology","tag-als","tag-amiotrofica","tag-amyotrophic","tag-criteria","tag-criterios","tag-diagnosis","tag-diagnostico","tag-el","tag-ela","tag-esclerosis","tag-escorial","tag-lateral","tag-neurology","tag-sclerosis"],"modified_by":"Guillermo Firman","_links":{"self":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/9","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/comments?post=9"}],"version-history":[{"count":4,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/9\/revisions"}],"predecessor-version":[{"id":9388,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/9\/revisions\/9388"}],"wp:attachment":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/media?parent=9"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/categories?post=9"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/tags?post=9"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}