{"id":90,"date":"2009-02-28T15:19:51","date_gmt":"2009-02-28T15:19:51","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/hemcvi\/"},"modified":"2025-05-14T19:11:58","modified_gmt":"2025-05-14T19:11:58","slug":"hemcvi","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/hemcvi\/","title":{"rendered":"Criterios Diagn\u00f3stico para Inmunodeficiencia Com\u00fan Variable (IDCV)"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>La inmunodeficiencia com\u00fan variable (IDCV) es una inmunodeficiencia rara caracterizada por bajos niveles de IgG s\u00e9rica, IgA y\/o IgM, con una p\u00e9rdida de producci\u00f3n de Ab. El diagn\u00f3stico se realiza con mayor frecuencia en adultos entre las edades de 20 y 40 a\u00f1os, pero se puede encontrar que tanto los ni\u00f1os como los adultos mayores tienen este defecto inmune.<!--more--><br \/>\n<strong>Criterios Diagn\u00f3stico<\/strong><\/p>\n<p style=\"font-weight: 400;\"><strong>Probable<\/strong><\/p>\n<p style=\"font-weight: 400;\">Paciente hombre o mujer que presenta disminuci\u00f3n marcada (al menos 2 SD por debajo del promedio para la edad) de IgG e IgA en suero y que cumplan todos de los siguientes criterios:<\/p>\n<ol style=\"font-weight: 400;\">\n<li>Comienzo de la inmunodeficiencia en mayores de 2 a\u00f1os de edad.<\/li>\n<li>Ausencia de isohemaglutininas y\/o pobre respuesta a vacunas.<\/li>\n<li>Causas definidas de hipogammaglobulinemia han sido excluidas.<\/li>\n<\/ol>\n<p style=\"font-weight: 400;\"><strong>Posible<\/strong><\/p>\n<p style=\"font-weight: 400;\">Paciente hombre o mujer que presenta disminuci\u00f3n marcada (al menos 2 SD por debajo del promedio para la edad) en uno de los isotipos mayores (IgM, IgG, e IgA) y que cumplan todos de los siguientes criterios::<\/p>\n<ol style=\"font-weight: 400;\">\n<li>Comienzo de la inmunodeficiencia en mayores de 2 a\u00f1os de edad.<\/li>\n<li>Ausencia de isohemaglutininas y\/o pobre respuesta a vacunas.<\/li>\n<li>Causas definidas de hipogammaglobulinemia han sido excluidas.<\/li>\n<\/ol>\n<p style=\"font-weight: 400;\"><strong>Diagn\u00f3stico Diferencial de Hipogammaglobulinemia<\/strong><\/p>\n<p style=\"font-weight: 400;\"><strong>Inducido por Drogas<\/strong><\/p>\n<ul style=\"font-weight: 400;\">\n<li>Agentes antimal\u00e1ricos<\/li>\n<li>Captopril<\/li>\n<li>Carbamazepina<\/li>\n<li>Glucocorticoides<\/li>\n<li>Fenclofenac<\/li>\n<li>Sales de oro<\/li>\n<li>Penicillamina<\/li>\n<li>Fenito\u00edna<\/li>\n<li>Sulfasalazina<\/li>\n<\/ul>\n<p style=\"font-weight: 400;\"><strong>Enfermedades gen\u00e9ticas<\/strong><\/p>\n<ul style=\"font-weight: 400;\">\n<li>Ataxia telangiectasia<\/li>\n<li>Formas autos\u00f3micas de inmunodeficiencia combinada severa<\/li>\n<li>Inmunodeficiencia hiper IgM<\/li>\n<li>Deficiencia de transcobalamina II e hipogammaglobulinemia<\/li>\n<li>Agammaglobulinemia\u00a0ligada al X<\/li>\n<li>Enfermedad linfoproliferativa ligada al X (asociada a EBV)<\/li>\n<li>Inmunodeficiencia combinada severa ligada al X<\/li>\n<li>Algunas enfermedades metab\u00f3licas<\/li>\n<\/ul>\n<p style=\"font-weight: 400;\"><strong>Anormalidades cromos\u00f3micas<\/strong><\/p>\n<ul style=\"font-weight: 400;\">\n<li>S\u00edndrome del cromosoma 18q2<\/li>\n<li>Monosom\u00eda 22<\/li>\n<li>Trisom\u00eda 8<\/li>\n<li>Trisom\u00eda\u00a021<\/li>\n<\/ul>\n<p style=\"font-weight: 400;\"><strong>Enfermedades infecciosas<\/strong><\/p>\n<ul style=\"font-weight: 400;\">\n<li>HIV<\/li>\n<li>Rub\u00e9ola cong\u00e9nita<\/li>\n<li>Infecci\u00f3n cong\u00e9nita con CMV<\/li>\n<li>Infecci\u00f3n cong\u00e9nita con\u00a0<em>Toxoplasma gondii<\/em><\/li>\n<li>Virus Epstein\u2013Barr<\/li>\n<\/ul>\n<p style=\"font-weight: 400;\"><strong>Enfermedades oncol\u00f3gicas<\/strong><\/p>\n<ul style=\"font-weight: 400;\">\n<li>Leucemia linfoc\u00edtica cr\u00f3nica<\/li>\n<li>Inmunodeficiencia con timoma<\/li>\n<li>Linfoma no Hodgkin<\/li>\n<li>Malignidad por c\u00e9lulas B<\/li>\n<\/ul>\n<p style=\"font-weight: 400;\"><strong>Enfermedades sist\u00e9micas<\/strong><\/p>\n<ul style=\"font-weight: 400;\">\n<li>Inmunodeficiencia causada por hipercatabolismo de inmunoglobulinas<\/li>\n<li>Inmunodeficiencia causada por p\u00e9rdida excesiva de inmunoglobulinas (nefrosis, quemaduras severas, linfangiectasia, diarrea severa)<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p style=\"font-weight: 400;\"><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol style=\"font-weight: 400;\">\n<li>Conley ME, Notarangelo LD, Etzioni A. Diagnostic criteria for primary immunodeficiencies. Representing PAGID (Pan-American Group for Immunodeficiency) and ESID (European Society for Immunodeficiencies). Clin Immunol. 1999 Dec;93(3):190-7.<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/10600329\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p style=\"font-weight: 400;\">Creado: Nov 03, 2007<\/p>\n<p><\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>La inmunodeficiencia com\u00fan variable (IDCV) es una inmunodeficiencia rara caracterizada por bajos niveles de IgG s\u00e9rica, IgA y\/o IgM, con una p\u00e9rdida de producci\u00f3n de Ab. El diagn\u00f3stico se realiza con mayor frecuencia en adultos entre las edades de 20 y 40 a\u00f1os, pero se puede encontrar que tanto los ni\u00f1os como los adultos mayores [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[171],"tags":[296,295,16,2018,14,1381,2017,293,290],"class_list":["post-90","post","type-post","status-publish","format-standard","hentry","category-hematology","tag-common","tag-comun","tag-criteria","tag-cvi","tag-diagnostic","tag-hematology","tag-immunodeficiency","tag-inmunodeficiencia","tag-variable"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Criterios Diagn\u00f3stico para Inmunodeficiencia Com\u00fan Variable (IDCV) - MedicalCRITERIA.com<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/medicalcriteria.com\/web\/hemcvi\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"[:es]Criterios Diagn\u00f3stico para Inmunodeficiencia Com\u00fan Variable (IDCV)[:en]Diagnostic Criteria for Common Variable Immunodeficiency (CVI)[:] - MedicalCRITERIA.com\" \/>\n<meta property=\"og:description\" content=\"La inmunodeficiencia com\u00fan variable (IDCV) es una inmunodeficiencia rara caracterizada por bajos niveles de IgG s\u00e9rica, IgA y\/o IgM, con una p\u00e9rdida de producci\u00f3n de Ab. El diagn\u00f3stico se realiza con mayor frecuencia en adultos entre las edades de 20 y 40 a\u00f1os, pero se puede encontrar que tanto los ni\u00f1os como los adultos mayores [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/medicalcriteria.com\/web\/hemcvi\/\" \/>\n<meta property=\"og:site_name\" content=\"MedicalCRITERIA.com\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/medicalcriteria\/\" \/>\n<meta property=\"article:published_time\" content=\"2009-02-28T15:19:51+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2025-05-14T19:11:58+00:00\" \/>\n<meta name=\"author\" content=\"Guillermo Firman\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Escrito por\" \/>\n\t<meta name=\"twitter:data1\" content=\"Guillermo Firman\" \/>\n\t<meta name=\"twitter:label2\" content=\"Tiempo de lectura\" \/>\n\t<meta name=\"twitter:data2\" content=\"3 minutos\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/hemcvi\\\/#article\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/hemcvi\\\/\"},\"author\":{\"name\":\"Guillermo Firman\",\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/#\\\/schema\\\/person\\\/ead6734a2f20659131388ba822c7078c\"},\"headline\":\"Criterios Diagn\u00f3stico para Inmunodeficiencia Com\u00fan Variable (IDCV)\",\"datePublished\":\"2009-02-28T15:19:51+00:00\",\"dateModified\":\"2025-05-14T19:11:58+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/hemcvi\\\/\"},\"wordCount\":699,\"publisher\":{\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/#organization\"},\"keywords\":[\"Common\",\"comun\",\"Criteria\",\"CVI\",\"Diagnostic\",\"hematology\",\"Immunodeficiency\",\"inmunodeficiencia\",\"Variable\"],\"articleSection\":[\"Hematology\"],\"inLanguage\":\"es\"},{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/hemcvi\\\/\",\"url\":\"https:\\\/\\\/medicalcriteria.com\\\/web\\\/hemcvi\\\/\",\"name\":\"[:es]Criterios Diagn\u00f3stico para Inmunodeficiencia Com\u00fan Variable (IDCV)[:en]Diagnostic Criteria for Common Variable Immunodeficiency (CVI)[:] - 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