{"id":9738,"date":"2022-06-10T18:55:53","date_gmt":"2022-06-10T18:55:53","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/?p=9738"},"modified":"2025-12-30T20:15:55","modified_gmt":"2025-12-30T20:15:55","slug":"rasmussen-encephalitis","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/rasmussen-encephalitis\/","title":{"rendered":"Criterios Cl\u00ednicos para Encefalitis de Rasmussen"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>La encefalitis de Rasmussen (ER) es un raro trastorno cerebral inflamatorio cr\u00f3nico que resulta en una neurodegeneraci\u00f3n progresiva en un hemisferio cerebral. El proceso inflamatorio se acompa\u00f1a de p\u00e9rdida progresiva de la funci\u00f3n del hemisferio afectado, asociada a epilepsia parcial resistente a f\u00e1rmacos. El diagn\u00f3stico se basa en una serie de argumentos cl\u00ednicos, electroencefalogr\u00e1ficos, radiol\u00f3gicos y bioqu\u00edmicos, sin ning\u00fan marcador formal espec\u00edfico, lo que hace complejo el diagn\u00f3stico de la enfermedad, especialmente en su fase inicial. Las convulsiones son refractarias a la medicaci\u00f3n anticonvulsiva (ASM) y a los tratamientos inmunomoduladores cl\u00e1sicos.<!--more--><\/p>\n<p><strong>Criterios cl\u00ednicos para encefalitis de Rasmussen<\/strong><\/p>\n<table style=\"border-collapse: collapse; width: 100%; height: 270px;\" border=\"1\">\n<tbody>\n<tr style=\"height: 24px;\">\n<td style=\"width: 20.0855%; height: 24px;\"><strong>Parte A<\/strong><\/td>\n<td style=\"width: 79.9145%; height: 24px;\"><strong>Necesidad 3\/3 = 5 criterios<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 48px;\">\n<td style=\"width: 20.0855%; height: 48px;\">Cl\u00ednicos<\/td>\n<td style=\"width: 79.9145%; height: 48px;\">Convulsiones focales cl\u00ednicas (\u00b1 epilepsia parcial continua) Y d\u00e9ficit(s) cortical(es) unilateral(es)<\/td>\n<\/tr>\n<tr style=\"height: 48px;\">\n<td style=\"width: 20.0855%; height: 48px;\">EEG<\/td>\n<td style=\"width: 79.9145%; height: 48px;\">Enlentecimiento unihemisf\u00e9rico \u00b1 actividad epileptiforme Y comienzo de convulsi\u00f3n focal unilateral<\/td>\n<\/tr>\n<tr style=\"height: 48px;\">\n<td style=\"width: 20.0855%; height: 48px;\">RNM<\/td>\n<td style=\"width: 79.9145%; height: 48px;\">Se\u00f1al hiperintensa en T2\/Flair de la sustancia gris o blanca, se\u00f1al hiperintensa o atrofia de la cabeza del caudado ipsilateral<\/td>\n<\/tr>\n<tr style=\"height: 24px;\">\n<td style=\"width: 20.0855%; height: 24px;\"><strong>Parte B<\/strong><\/td>\n<td style=\"width: 79.9145%; height: 24px;\"><strong>Necesita 2\/3<\/strong><\/td>\n<\/tr>\n<tr style=\"height: 27px;\">\n<td style=\"width: 20.0855%; height: 27px;\">Cl\u00ednicos<\/td>\n<td style=\"width: 79.9145%; height: 27px;\">Epilepsia parcial continua o d\u00e9ficit(s) cortical(es) unilateral(es) progresivo(s)<sup>a<\/sup><\/td>\n<\/tr>\n<tr style=\"height: 27px;\">\n<td style=\"width: 20.0855%; height: 27px;\">RNM<\/td>\n<td style=\"width: 79.9145%; height: 27px;\">Atrofia cortical focal unihemisf\u00e9rica progresiva<sup>a<\/sup><\/td>\n<\/tr>\n<tr style=\"height: 24px;\">\n<td style=\"width: 20.0855%; height: 24px;\">Histopatolog\u00eda<\/td>\n<td style=\"width: 79.9145%; height: 24px;\">Encefalitis dominada por c\u00e9lulas T con c\u00e9lulas microgliales activadas (biopsia cerebral)<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p>El paciente debe cumplir con los criterios A o B. <sup>a<\/sup> Progresivo significa que son necesarios al menos dos ex\u00e1menes cl\u00ednicos secuenciales y estudios de resonancia magn\u00e9tica para concluir.<\/p>\n<p>&nbsp;<\/p>\n<p><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li>Villeneuve N, L\u00e9pine A, Girard N, Guedj E, Daquin G. Rasmussen&#8217;s encephalitis: Early diagnostic criteria in children. Rev Neurol (Paris). 2022 May 11:S0035-3787(22)00583-5. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/35568516\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<li>Cay-Martinez KC, Hickman RA, McKhann Ii GM, Provenzano FA, Sands TT. Rasmussen Encephalitis: An Update. Semin Neurol. 2020 Apr;40(2):201-210. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/32185790\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Jun 06, 2022.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>La encefalitis de Rasmussen (ER) es un raro trastorno cerebral inflamatorio cr\u00f3nico que resulta en una neurodegeneraci\u00f3n progresiva en un hemisferio cerebral. El proceso inflamatorio se acompa\u00f1a de p\u00e9rdida progresiva de la funci\u00f3n del hemisferio afectado, asociada a epilepsia parcial resistente a f\u00e1rmacos. El diagn\u00f3stico se basa en una serie de argumentos cl\u00ednicos, electroencefalogr\u00e1ficos, radiol\u00f3gicos [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[2],"tags":[490,1401,16,15,253,252,2492],"class_list":["post-9738","post","type-post","status-publish","format-standard","hentry","category-neurology","tag-clinical","tag-clinicos","tag-criteria","tag-criterios","tag-encefalitis","tag-encephalitis","tag-rasmussen"],"modified_by":"Guillermo Firman","_links":{"self":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/9738","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/comments?post=9738"}],"version-history":[{"count":9,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/9738\/revisions"}],"predecessor-version":[{"id":9880,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/9738\/revisions\/9880"}],"wp:attachment":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/media?parent=9738"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/categories?post=9738"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/tags?post=9738"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}