{"id":9755,"date":"2022-07-06T15:41:44","date_gmt":"2022-07-06T15:41:44","guid":{"rendered":"https:\/\/medicalcriteria.com\/web\/?p=9755"},"modified":"2025-12-30T20:14:39","modified_gmt":"2025-12-30T20:14:39","slug":"leukemia-acml","status":"publish","type":"post","link":"https:\/\/medicalcriteria.com\/web\/es\/leukemia-acml\/","title":{"rendered":"Criterios Diagn\u00f3stico de Leucemia Mieloide Cr\u00f3nica At\u00edpica (LMCa)"},"content":{"rendered":"<div class=\"7ca9444b8380138fe077da07353677a4\" data-index=\"1\" style=\"float: none; margin:0px 0 0px 0; text-align:center;\">\n<script async src=\"https:\/\/pagead2.googlesyndication.com\/pagead\/js\/adsbygoogle.js\"><\/script>\r\n<!-- MC 2019- Horizontal -->\r\n<ins class=\"adsbygoogle\"\r\n     style=\"display:block\"\r\n     data-ad-client=\"ca-pub-0127150553352455\"\r\n     data-ad-slot=\"3806776041\"\r\n     data-ad-format=\"auto\"\r\n     data-full-width-responsive=\"true\"><\/ins>\r\n<script>\r\n     (adsbygoogle = window.adsbygoogle || []).push({});\r\n<\/script>\n<\/div>\n<p>La leucemia miel\u00f3gena cr\u00f3nica at\u00edpica (LMCa), BCR\/ABL1 negativo, es un trastorno raro clasificado en la categor\u00eda de neoplasias mielodispl\u00e1sicas\/mieloproliferativas (SMD\/NMP), seg\u00fan la revisi\u00f3n de 2016 de la clasificaci\u00f3n de la Organizaci\u00f3n Mundial de la Salud (OMS) de neoplasias mieloides y leucemias agudas. Es, por definici\u00f3n, un trastorno clonal BCR-ABL1 negativo que comparte caracter\u00edsticas mielodispl\u00e1sicas y mieloproliferativas.<\/p>\n<p><!--more--><\/p>\n<p><strong>Criterios Diagn\u00f3stico de Leucemia Mieloide Cr\u00f3nica At\u00edpica (LMCa)<\/strong><\/p>\n<table style=\"border-collapse: collapse; width: 100%;\" border=\"1\">\n<tbody>\n<tr>\n<td style=\"width: 25.2137%;\"><strong>Carcter\u00edstica<\/strong><\/td>\n<td style=\"width: 74.7863%;\"><strong>OMS 2016<\/strong><\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Cromosoma Filadelfia<\/td>\n<td style=\"width: 74.7863%;\">Ausente<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">BCR\/ABL1<\/td>\n<td style=\"width: 74.7863%;\">Ausente<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Leucocitosis<\/td>\n<td style=\"width: 74.7863%;\">Persistente (\u226513&#215;10<sup>9<\/sup>\/L)<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Recuento de bas\u00f3filos<\/td>\n<td style=\"width: 74.7863%;\">&lt;2%<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Recuento de monocitos<\/td>\n<td style=\"width: 74.7863%;\">&lt;10% de leucocitos<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Displasia multilinaje<\/td>\n<td style=\"width: 74.7863%;\">Puede haber diseritropoyesis y dismegacariopoyesis<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Disgranulopoyesis<\/td>\n<td style=\"width: 74.7863%;\">Presente<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Granulocitos inmaduros<\/td>\n<td style=\"width: 74.7863%;\">\u2265 10% leucocitos<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Blastos<\/td>\n<td style=\"width: 74.7863%;\">&lt;20% (sangre y m\u00e9dula \u00f3sea)<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Celularidad en m\u00e9dula \u00f3sea<\/td>\n<td style=\"width: 74.7863%;\">M\u00e9dula \u00f3sea hipercelular<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Otras caracter\u00edsticas moleculares<\/td>\n<td style=\"width: 74.7863%;\">Sin reordenamientos de PDGFRA, PDGFRB, FGFR1, y PCM1-JAK2<br \/>\n\u00c9nfasis en cambios moleculares (ETNK1, SETBP1)<\/td>\n<\/tr>\n<tr>\n<td style=\"width: 25.2137%;\">Otros factores<\/td>\n<td style=\"width: 74.7863%;\">No se cumplen los criterios de la OMS para otras neoplasias mieloproliferativas<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p>&nbsp;<\/p>\n<p><strong>Bibliograf\u00eda:<\/strong><\/p>\n<ol>\n<li>Diamantopoulos PT, Viniou NA. Atypical Chronic Myelogenous Leukemia, BCR-ABL1 Negative: Diagnostic Criteria and Treatment Approaches. Front Oncol. 2021 Nov 17;11:722507. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/34868917\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<li>Belkhair J, Raissi A, Elyahyaoui H, Ameur MA, Chakour M. Atypical chronic myeloid leukemia BCR-ABL 1 negative: A case report and literature review. Leuk Res Rep. 2019 May 25;12:100172. <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/31194134\/\" target=\"_blank\" rel=\"noopener\">[Medline]<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<p>Creado Jun 24, 2022.<\/p>\n\n<div style=\"font-size: 0px; height: 0px; line-height: 0px; margin: 0; padding: 0; clear: both;\"><\/div>","protected":false},"excerpt":{"rendered":"<p>La leucemia miel\u00f3gena cr\u00f3nica at\u00edpica (LMCa), BCR\/ABL1 negativo, es un trastorno raro clasificado en la categor\u00eda de neoplasias mielodispl\u00e1sicas\/mieloproliferativas (SMD\/NMP), seg\u00fan la revisi\u00f3n de 2016 de la clasificaci\u00f3n de la Organizaci\u00f3n Mundial de la Salud (OMS) de neoplasias mieloides y leucemias agudas. Es, por definici\u00f3n, un trastorno clonal BCR-ABL1 negativo que comparte caracter\u00edsticas mielodispl\u00e1sicas y [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_lmt_disableupdate":"no","_lmt_disable":"no","_exactmetrics_skip_tracking":false,"_exactmetrics_sitenote_active":false,"_exactmetrics_sitenote_note":"","_exactmetrics_sitenote_category":0,"footnotes":""},"categories":[171],"tags":[2498,2495,2497,146,16,15,145,14,13,2346,2351,2496,2347,2284],"class_list":["post-9755","post","type-post","status-publish","format-standard","hentry","category-hematology","tag-acml","tag-atipica","tag-atypical","tag-chronic","tag-criteria","tag-criterios","tag-cronica","tag-diagnostic","tag-diagnostico","tag-leucemia","tag-leukemia","tag-lmca","tag-mieloide","tag-myeloid"],"modified_by":"Guillermo Firman","_links":{"self":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/9755","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/comments?post=9755"}],"version-history":[{"count":7,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/9755\/revisions"}],"predecessor-version":[{"id":9769,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/posts\/9755\/revisions\/9769"}],"wp:attachment":[{"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/media?parent=9755"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/categories?post=9755"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/medicalcriteria.com\/web\/es\/wp-json\/wp\/v2\/tags?post=9755"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}