La dermatomiositis es una enfermedad idiopática, que incluye miopatía inflamatoria y manifestaciones cutáneas características; la polimiositis incluye la miopatía inflamatoria sin signos cutáneos.
criterios
Diagnosis of Obstructive Sleep Apnea (OSA) in Adults and Children
Obstructive sleep apnea syndrome (OSAS) is defined as repeated episodes of obstructive apneas and hypopneas during sleep, frequently followed by transient hemoglobin desaturation (hypoxemia) and unconscious (EEG) arousals.
Diagnostic Criteria for Progressive Multifocal Leukoencephalopathy (PML)
Progressive multifocal leukoencephalopathy (PML) is a demyelinating disease of the central nervous system caused by the reactivation of a ubiquitous polyomavirus JC (JCV). PML was for many years a rare disease occurring only in patients with underlying severe impaired immunity.
Diagnostic Criteria for Sporadic Creutzfeldt-Jakob Disease (sCJD)
Classic Creutzfeldt-Jakob Disease (CJD) is a human prion disease. It is a neurodegenerative disorder with characteristic clinical and diagnostic features. This disease is rapidly progressive and always fatal. Infection with this disease leads to death, usually within 1 year of onset of illness. The criteria for clinical diagnosis plus the CSF real-time quaking-induced conversion (RT-QuIC) accurately identifies patients with sCJD (sensitivity 97%, specificity 99%).
Electrodiagnostic Criteria for Chronic Inflammatory Demyelinating Polyradiculoneuropathy (CIDP)
These criteria are applied by testing the median, ulnar (stimulated below the elbow), peroneal (stimulated below the fibular head), and tibial nerves on one side of the body. During testing, limb temperature should be no less than 33°C at the palm and no less than 30°C at the external malleolus.
Diagnostic Criteria for Autoimmune Lymphoproliferative Syndrome (ALPS)
Autoimmune lymphoproliferative syndrome (ALPS) is characterized by dysregulation of the immune system due to an inability to regulate lymphocyte homeostasis through the process of lymphocyte apoptosis (a form of programmed cell death). The consequences of this include lymphoproliferative disease, manifested by lymphadenopathy, hepatomegaly, splenomegaly, and an increased risk of lymphoma, as well as autoimmune disease, typically involving blood cells.
Diagnostic Criteria for Thyroid Storm
Burch and Wartofsky have delineated a point system assessing degrees of dysfunction in various systems (thermoregulatory, central nervous, gastrointestinal, and cardiovascular).
Diagnostic Criteria for Small Fibre Neuropathy (SFN)
Small fiber neuropathy manifests in a variety of different diseases and often results in symptoms of burning pain, shooting pain, allodynia, and hyperesthesia.
Clinical Criteria for Bell’s Palsy (Idiopathic Facial Nerve Paralysis)
Bell’s palsy is a peripheral palsy of the facial nerve that results in muscle weakness on one side of the face.
Diagnostic Criteria for Refractory Ascites
Refractory ascites is defined as ascites that does not recede or that recurs shortly after therapeutic paracentesis, despite sodium restriction and diuretic treatment.